Ola kinoMaʻi a me nā kūlana

Bulbar maʻi pale: symptoms, kumu, lapaʻau

Bulbar maʻi pale i kapaia bulbar lolo - he sublingual poino maʻi pale, glossopharyngeal a me vagal cranial nā aʻalolo, ka nucleus o i i aia i loko o ka medulla oblongata. Bulbar maʻi pale ia lŘlŘ iʻelua papa (emi ma hoʻokahi-kapakahi) poino nuclei X, IX, XI a me XII cranial nā aʻalolo, caudal i ka pili pae, a i loko iho i loko o ka medulla oblongata. Eia hou kekahi, pōʻino i hooleiiaʻi mawaho aa a me nā aʻalolo nui ilpko o loko o ka cranial lua, a ma o aku o.

I ka bulbar maʻi pale ia lŘlŘ flaccid lōlō o ka puu nāʻiʻo, lehelehe, olelo, palupalu kīleo, epiglottis a me nā kaula vocal. I ka hopena o keia mea he lōlō dysphagia (moni 'ia kāna hana hana) a me ka dysarthria (mai ka pioloke o ka olelo). Bulbar dysarthria ua wehewehe aku ma ka nawaliwali a me ka puha leo, a hiki i ka piha aphonia, malaila twang a "blur" kani. Ka puana o leokanipū mea kani-pu ole, i loko o ka wahi o ka articulation (apicals, labial, velar) a me ka papa hana no ka ho okumu i (kau, occlusives, palupalu, paa) i ka iaʻano, a me nā vowels - kākaʻikahi distinguishable mai kekahi i kekahi. Olelo i loko o nā mea maʻi me kaʻike, o "bulbar maʻi pale" ka meheu o ia, a nui loa nā mea maʻi māluhiluhi. Ke kaumaha ma muli o ka oolea o ke Muscle paresis a me kona prevalence bulbar dysarthria maʻi pale paha e global, hapa paha e wae.

Nā mea maʻi me ka bulbar lolo ka hakui o hiki ke kinowai ai ka ai, e like me hikiʻole i ka paka moni 'ia Joshua, ma ka loa hoopii, e hoomanawanui i hoʻomōhala kāna hana o cardiac haʻawina a me ka hanu nā rhythms mea pinepine hiki aku i ka make. No ia mea, ia mea paʻakikī nui 'eleu pilikia mālama i nā mea maʻi i kēia maʻi pale. Ua mea e hoʻopau i ka hoʻoweliweli 'ana i ke ola, a mahope ka halihali ana i ka hana kūikawā' inikua wahi uku paha.

Bulbar maʻi pale ua wehewehe aku ma na kēia mau maʻi:

- aaiaoe maʻi, e like me Kennedy ka maʻi a me ka porphyria;

- vascular maʻi (myocardial medulla);

- siringobulbiya, Hawaii neuron maʻi;

- hoʻoʻino a infectious maʻi (Lyme maʻi, Guillain-Barre maʻi pale);

- Ka maʻi 'aʻai (glioma, lolo anei i).

Ke kumu no ka diagnosing bulbar lōlō o ka 'ike ano hoailona a me lapaʻau symptoms. Ka loa ike loea ki ina hana like no kaʻike, o keia maʻi nā electromyographyʻikepili a me ka pololei ninaninau o ka oropharynx.

Aia bulbar a me ka pseudobulbar syndromes. Ka papa likeʻole ma waena o ia moe ana ma ka oiaio i ka pseudobulbar maʻi pale maʻi lōlō nāʻiʻo mai i lilo atrophied, oa lōlō meaʻike ākea,ʻaʻohe fibrillary twitch nāʻiʻo o ke elelo, a me ka naoh o degeneration. Pseudobulbar lolo ua pinepine pu e hao wale mai kahea ana a me kaʻakaʻaka, a i ke kumu ma ka hui ole ma waena o Central subcortical aka wahi a me ka wauke. Pseudobulbar lolo , e like bulbar ole i apnea (cessation o ka hanu 'ana), a me ka naau pāpana haunaele. Ua Ua mālama i loko o ka lula 'eiei? Lolo lesions me vascular, infectious, traumatic a intoxication Kin.

Bulbar maʻi pale: lapaau.

bulbar lōlō o iapaau ana ua pahunaʻano nui ma ke kāpaeʻana i ka nń ku maʻi a me ka uku oihana i hihia hoʻi. E hoʻoikaika moni 'ia oihana i häʻawi mai ai iä ai' e like me glutamicʻakika, Neostigmine, nootropics, galantamine a me nā wikamina, a ma mahuahua salivation - lāʻau atropine. Hanai ana oia i mau e hoomanawanui i ua i ma kaʻimi, 'o ia hoʻi, enterally. I Ina o ka 'aʻe' ana i ka ÷ naehana hanu kuleana pili i ua häʻawi mai ai iä ka ventilator.

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