Ola kinoMaʻi a me nā kūlana

Eisenmenger maʻi pale: symptoms. Eisenmenger maʻi pale a me ka hāpai keiki. Hoʻomanawanui iki mai me Eisenmenger maʻi pale

Demonstrable holomua ma ka lapaau ma luna o ka mau makahiki i hala iho nei i i alakai i ka oi mahuahua i loko o ke ola expectancy, a me ka hoʻopau o cardiac pathologies. Eia hou, ma ka huli ana o XIX-XX kenekulia, ua ho'ākāka 'ia ma nä känaka' epekema he nui hou maʻi. Nā kumu no kekahi o ia nō kai koe mai he mea pohihihi, me ka symptoms - blurred, a me ka hana i loa paʻakikī. Eisenmenger maʻi pale, i kapaia ma ka inoa o ka'Aukekulia pediatrician a me ka cardiologist, hiki ole ke manaoia, he pono ole. Pohihihi keia pathology loaa ka piha hōʻike ma kahi o 100 mau makahiki aku nei. Eia naʻe, hiki i keia la, mai i ke kamailio e pili ana i ka maopopo pau loa o kona etiology.

kekahi mau 'ike

Maʻi pale (kekahi manawa, kapaʻia eiiieaena) Eisenmenger - he pilikia loa pathology, hiki i ka pulmonary a me ka cardiac kahua. Cardiac maʻi ua wehewehe aku ma ka hoʻohui pūʻia ventricular septal kina , a me ka hypertension. maʻi ulu hiki aku ai i mahuahua ka puʻuwai a me ka hoʻohuikau i loko o ka pulmonary holo. I ka hopena o ka shunt, i mea kuleana no ke koko hoʻokomo akula ka pono, e haʻalele, a aʻe ka mea maʻamau keʻano o ka hanaʻana hemodynamics.

Nō hoʻi, ke manaʻo o Eisenmenger maʻi pale nā kekahi naau mai, wehewehe aku ma ka hamama atrioventricular Canal, a iaoaioa ductus arteriosus, i ke alo o ka hoʻokahi wale nō ventricle. I waena o nā mea maʻi me ka'āno'ē ventricular septal pathology ua diagnosed i loko o 10% o ka hihia. Ma ka 'ole o ka congenital mā ka papa kuhikuhi kino nāʻiʻo Eisenmenger eiiieaena ka 3%.

Kumu o ka maʻi pale ulu

Single kumu o ka hooulu ana o ka maʻi, hiki ole ke kapa kahuna lapaau. Eia naʻe, loaʻa nō i ka helu o ka etiological aʻe e hoomahuahua i ka likelihood o ka poe keiki a me Eisenmenger maʻi pale:

  1. Hereditary predisposition. Aʻe 'ana ma ka'ōewe pae hiki ke hele mai ka makua i ke keiki, ma laila e kauoha ana i ka māhuahua wale o ka ulu naau maʻi.
  2. ? Aneie aʻe:
  • intoxication o ka fetus ma utero;
  • hooloihiia waiū i ka electromagnetic a pāhawewe;
  • maʻi infectious mai o ka makua;
  • ʻaoʻao 'ole o ka lapaʻauʻia a me dietary kumukanawai a hoʻohana' ia e nā wāhine i hāpai keiki.

Mau kumumea i ole typical pono no Eisenmenger maʻi pale, akā, ma ka kumumanaʻo o ka mea hiki ia i ke kumu o nā pathologies, a me kēia kekahi.

E like me ka maʻi e hoʻomōhala ana i?

Hoʻomanawanui iki mai me Eisenmenger maʻi pale ana mai hoi hoohewa aku ola pilikia o. No laila, i kakahiaka nuiʻike, mea,ʻaʻole e mau ana e hiki. Ke kamaiki attaches mua uku 'maomeka, akā, ma hope o kekahi manawa o ka maʻi hoike mai ai ia ia iho. Kūloko kumu waiwai menemene, ka cardiac nenoaiu ua nele. He aha ka Eisenmenger maʻi pale symptoms?

  1. Hoomahuahua ae la lakou nawaliwali,ʻino ma hope o hoʻokō '.
  2. Pain ma kaʻaoʻao hema o ka pahu.
  3. Ulu ao, ahinahina o ka ili.
  4. Noho'na makaainana i ulu syncope.
  5. Ino o ka cough me ka koko hookuuia.

Oia symptoms i no e aole loa a pau. Ka maʻi pale no ka lōʻihi manawa hiki hoʻomōhala koke. Inā he pediatrician i poʻe luna no ka keiki, paipai i ka kekahi, he hou ka ninaninau i loko o ka cardiology iwaena konu, ka mea e ole e malama ole.

Prenatal mālama i maʻi

Lūkini kauka manaʻo i ka Eisenmenger maʻi pale a me ka hāpai keiki i incompatible. No laila, ma kekahi kahua o ka wahine, e i ka abortion ua paipai. Lākou Western nā hoapili manao ole ia. E like me ia ia lakou, noho pomaikai hanauna hilinai ma kaʻaeʻana me ka lākou o nā rula a me nā koi.

Ka mua wahine e hospitalization no ka mea a pau wā o ka hāpai keiki. Ma ka haukapila, kauka pono i mau kanaka hoʻoponopono i ke kūlana o ka fetus, a, e ana i ka puʻe i loko o ka pulmonary capillaries. Ma ka hoailona mua o ka pokole o ka hanu - ka oxygen ea paha. E hoʻomaka ana, mai ka lua o ka trimester ia lapaau coagulants. A mau lā ma mua o ka manaʻo lā o ka hanana o ke keiki paipai kŰia Inc o digitalis, e malama i cardiac kahua. Delivery mea hiki wale nō i loko o ka kūlohelohe alanui.

Inā he wahine e noho ana me na koi a pau o ka poe kumu, ka pahiki o ka maikaʻi hope no ke keiki o 50-90%. Ke kēla mea,ʻaʻole like conducive i ka makuwahine. I ka wā i hoʻoholo 'ia ma ka mau nō lā hoʻi o ka hāpai keiki, e manaʻo ke kumu, he wahine e pili ana i ka Loaʻaʻia ka pilikia.

Lapaʻau o keia hookolokolo ana

Haʻi'ōlelo Inc no nā mea maʻi me Eisenmenger maʻi pale mea hiki ole ke manao wale me ke kupaianaha ninaninau. Ua hiki wale e hele ma ka hana kūikawā nā keʻena lāʻau lapaʻau a me ka lako a kūpono. Inā 'oe hāʻupu aʻe i kēia pathology loiloi polokalamu ana mai nā':

  • umauma radiograph (olelo loli ma pulmonary artery a me contours o ka naau);
  • angiography (vascular study);
  • ECG (kuhikuhi i hunaia naau pāpana ka haunaele);
  • Echocardiography (visualization o pathological loli i loko o nā paia o nā ventricles);
  • cardiac catheterization (ka auhau ana o ka mai, a me ka 'ano o nā palapū, i ka ana o ka laulā kiko'î o ka papa kuhikuhiE nāʻiʻo).

Palena pauʻike, Ua OAXA i loko o nā mea maʻi a pau me kēia Eisenmenger maʻi pale. Pentad Fallot, arteries stenosis, iaoaioa ductus arteriosus - he pōkole papa inoa o pathologies, e hookaawale ia.

Inc nā loina

Makeʻe kulana lapaʻau o nā mea maʻi mea hiki, akā,ʻaʻole ka maiau. Ma ka kekahi lima, me ka hoʻohana 'ana iʻoki lāʻau lapaʻau' uao, aole ia e mau paka maikaʻi hopena. No laila, i kēia lā kauka i increasingly io i ka hui pu ana, ka hoʻolālā.

Nā mea maʻi me ka haʻi lapaʻau kiʻi, a mahuahua hematocrit hoonohoia phlebotomy. Ke kaʻina hana Ua hai mai i ka ekolu manawa o ka makahiki, i ka mea ia manawa ia mea mau Kuleana e kanaka hoʻoponopono koko hao kiko'î. Oxygen ma Inc a me ka anticoagulant lapaʻau ua kākaʻikahi hoʻohana ', aole i ponoʻole. I ka papa kuhikuhiE drawback o kēia mau kaʻina hana ua noʻonoʻo i ka nui helu o kaʻaoʻao 'ole, i ka mea nui i waena o i mea he hemorrhagic diathesis. No hoi, e hoomanawanui i hoakaka ai '. "Epoprostenol" a me ka "Treprostinil"? Ienoai aa hemodynamics a "Traklir" ho'ēmi i kā vascular e kū'ē'ē mai.

ʻoki kino ua lawe mai i loko o nā Lolina: ka implantation o ka pacemaker, ea kina MPP. A lohe o Eisenmenger maʻi pale hana hiki me ka nui loa hoʻoikaika i ka prognosis o ka maʻi. Inā mau nohoʻana i ineffective, hiki wale nō ke kōkua i ka i ka wā hoʻokahi transplantation o na maʻiʻaʻai a me ka naau. Transplantationʻoki kino o ke koa huikau, pono nui kālā koina. Ma ka kekahi lima, ka mea, 'aʻole e hoʻopau i ka pilikia o complications. I ka wā i nā pāʻoihana,ʻo nā nīnau mea straightforward, papalua transplant ke hoola i ka ola. Prior i kona manaʻo mea pono i kekahi, i ka luna '' inikua ninaninau.

Pehea e hoʻomanawanui iki mai me Eisenmenger maʻi pale?

Kanaka, ka poe i, e hana me keia cardiac maʻi, pinepine i kaʻeleu ola. Naʻe, ka mea, i ke mau e hele i ke kauka, a ke kanaka hoʻoponopono ola nā hoailona. Oia nā mea maʻi e pale aku dehydration, hooloihi ae i waiū e kiʻekiʻena infectious maʻi. He nui, e haawi aku iʻinoʻano a me ka lawe lapaʻauʻia i hiki i kahe ana ke koko. Inā ka hoʻomanawanui penei kauka mau kauoha, i ka pahiki o ka manawa kūpono e alakai i ka maʻamau ola, piʻi pū. I ole ia, ke koko oxygen ma kaʻilikai i haule i ka noho pilikia pae i alakai i ka make.

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