Ola kino, Maʻi a me nā kūlana
Eisenmenger maʻi pale: symptoms. Eisenmenger maʻi pale a me ka hāpai keiki. Hoʻomanawanui iki mai me Eisenmenger maʻi pale
Demonstrable holomua ma ka lapaau ma luna o ka mau makahiki i hala iho nei i i alakai i ka oi mahuahua i loko o ke ola expectancy, a me ka hoʻopau o cardiac pathologies. Eia hou, ma ka huli ana o XIX-XX kenekulia, ua ho'ākāka 'ia ma nä känaka' epekema he nui hou maʻi. Nā kumu no kekahi o ia nō kai koe mai he mea pohihihi, me ka symptoms - blurred, a me ka hana i loa paʻakikī. Eisenmenger maʻi pale, i kapaia ma ka inoa o ka'Aukekulia pediatrician a me ka cardiologist, hiki ole ke manaoia, he pono ole. Pohihihi keia pathology loaa ka piha hōʻike ma kahi o 100 mau makahiki aku nei. Eia naʻe, hiki i keia la, mai i ke kamailio e pili ana i ka maopopo pau loa o kona etiology.
kekahi mau 'ike
Maʻi pale (kekahi manawa, kapaʻia eiiieaena) Eisenmenger - he pilikia loa pathology, hiki i ka pulmonary a me ka cardiac kahua. Cardiac maʻi ua wehewehe aku ma ka hoʻohui pūʻia ventricular septal kina , a me ka hypertension. maʻi ulu hiki aku ai i mahuahua ka puʻuwai a me ka hoʻohuikau i loko o ka pulmonary holo. I ka hopena o ka shunt, i mea kuleana no ke koko hoʻokomo akula ka pono, e haʻalele, a aʻe ka mea maʻamau keʻano o ka hanaʻana hemodynamics.
Nō hoʻi, ke manaʻo o Eisenmenger maʻi pale nā kekahi naau mai, wehewehe aku ma ka hamama atrioventricular Canal, a iaoaioa ductus arteriosus, i ke alo o ka hoʻokahi wale nō ventricle. I waena o nā mea maʻi me ka'āno'ē ventricular septal pathology ua diagnosed i loko o 10% o ka hihia. Ma ka 'ole o ka congenital mā ka papa kuhikuhi kino nāʻiʻo Eisenmenger eiiieaena ka 3%.
Kumu o ka maʻi pale ulu
Single kumu o ka hooulu ana o ka maʻi, hiki ole ke kapa kahuna lapaau. Eia naʻe, loaʻa nō i ka helu o ka etiological aʻe e hoomahuahua i ka likelihood o ka poe keiki a me Eisenmenger maʻi pale:
- Hereditary predisposition. Aʻe 'ana ma ka'ōewe pae hiki ke hele mai ka makua i ke keiki, ma laila e kauoha ana i ka māhuahua wale o ka ulu naau maʻi.
- ? Aneie aʻe:
- intoxication o ka fetus ma utero;
- hooloihiia waiū i ka electromagnetic a pāhawewe;
- maʻi infectious mai o ka makua;
- ʻaoʻao 'ole o ka lapaʻauʻia a me dietary kumukanawai a hoʻohana' ia e nā wāhine i hāpai keiki.
Mau kumumea i ole typical pono no Eisenmenger maʻi pale, akā, ma ka kumumanaʻo o ka mea hiki ia i ke kumu o nā pathologies, a me kēia kekahi.
E like me ka maʻi e hoʻomōhala ana i?
Hoʻomanawanui iki mai me Eisenmenger maʻi pale ana mai hoi hoohewa aku ola pilikia o. No laila, i kakahiaka nuiʻike, mea,ʻaʻole e mau ana e hiki. Ke kamaiki attaches mua uku 'maomeka, akā, ma hope o kekahi manawa o ka maʻi hoike mai ai ia ia iho. Kūloko kumu waiwai menemene, ka cardiac nenoaiu ua nele. He aha ka Eisenmenger maʻi pale symptoms?
- Hoomahuahua ae la lakou nawaliwali,ʻino ma hope o hoʻokō '.
- Pain ma kaʻaoʻao hema o ka pahu.
- Ulu ao, ahinahina o ka ili.
- Noho'na makaainana i ulu syncope.
- Ino o ka cough me ka koko hookuuia.
Oia symptoms i no e aole loa a pau. Ka maʻi pale no ka lōʻihi manawa hiki hoʻomōhala koke. Inā he pediatrician i poʻe luna no ka keiki, paipai i ka kekahi, he hou ka ninaninau i loko o ka cardiology iwaena konu, ka mea e ole e malama ole.
Prenatal mālama i maʻi
Lūkini kauka manaʻo i ka Eisenmenger maʻi pale a me ka hāpai keiki i incompatible. No laila, ma kekahi kahua o ka wahine, e i ka abortion ua paipai. Lākou Western nā hoapili manao ole ia. E like me ia ia lakou, noho pomaikai hanauna hilinai ma kaʻaeʻana me ka lākou o nā rula a me nā koi.
Ka mua wahine e hospitalization no ka mea a pau wā o ka hāpai keiki. Ma ka haukapila, kauka pono i mau kanaka hoʻoponopono i ke kūlana o ka fetus, a, e ana i ka puʻe i loko o ka pulmonary capillaries. Ma ka hoailona mua o ka pokole o ka hanu - ka oxygen ea paha. E hoʻomaka ana, mai ka lua o ka trimester ia lapaau coagulants. A mau lā ma mua o ka manaʻo lā o ka hanana o ke keiki paipai kŰia Inc o digitalis, e malama i cardiac kahua. Delivery mea hiki wale nō i loko o ka kūlohelohe alanui.
Inā he wahine e noho ana me na koi a pau o ka poe kumu, ka pahiki o ka maikaʻi hope no ke keiki o 50-90%. Ke kēla mea,ʻaʻole like conducive i ka makuwahine. I ka wā i hoʻoholo 'ia ma ka mau nō lā hoʻi o ka hāpai keiki, e manaʻo ke kumu, he wahine e pili ana i ka Loaʻaʻia ka pilikia.
Lapaʻau o keia hookolokolo ana
Haʻi'ōlelo Inc no nā mea maʻi me Eisenmenger maʻi pale mea hiki ole ke manao wale me ke kupaianaha ninaninau. Ua hiki wale e hele ma ka hana kūikawā nā keʻena lāʻau lapaʻau a me ka lako a kūpono. Inā 'oe hāʻupu aʻe i kēia pathology loiloi polokalamu ana mai nā':
- umauma radiograph (olelo loli ma pulmonary artery a me contours o ka naau);
- angiography (vascular study);
- ECG (kuhikuhi i hunaia naau pāpana ka haunaele);
- Echocardiography (visualization o pathological loli i loko o nā paia o nā ventricles);
- cardiac catheterization (ka auhau ana o ka mai, a me ka 'ano o nā palapū, i ka ana o ka laulā kiko'î o ka papa kuhikuhiE nāʻiʻo).
Palena pauʻike, Ua OAXA i loko o nā mea maʻi a pau me kēia Eisenmenger maʻi pale. Pentad Fallot, arteries stenosis, iaoaioa ductus arteriosus - he pōkole papa inoa o pathologies, e hookaawale ia.
Inc nā loina
Makeʻe kulana lapaʻau o nā mea maʻi mea hiki, akā,ʻaʻole ka maiau. Ma ka kekahi lima, me ka hoʻohana 'ana iʻoki lāʻau lapaʻau' uao, aole ia e mau paka maikaʻi hopena. No laila, i kēia lā kauka i increasingly io i ka hui pu ana, ka hoʻolālā.
Nā mea maʻi me ka haʻi lapaʻau kiʻi, a mahuahua hematocrit hoonohoia phlebotomy. Ke kaʻina hana Ua hai mai i ka ekolu manawa o ka makahiki, i ka mea ia manawa ia mea mau Kuleana e kanaka hoʻoponopono koko hao kiko'î. Oxygen ma Inc a me ka anticoagulant lapaʻau ua kākaʻikahi hoʻohana ', aole i ponoʻole. I ka papa kuhikuhiE drawback o kēia mau kaʻina hana ua noʻonoʻo i ka nui helu o kaʻaoʻao 'ole, i ka mea nui i waena o i mea he hemorrhagic diathesis. No hoi, e hoomanawanui i hoakaka ai '. "Epoprostenol" a me ka "Treprostinil"? Ienoai aa hemodynamics a "Traklir" ho'ēmi i kā vascular e kū'ē'ē mai.
ʻoki kino ua lawe mai i loko o nā Lolina: ka implantation o ka pacemaker, ea kina MPP. A lohe o Eisenmenger maʻi pale hana hiki me ka nui loa hoʻoikaika i ka prognosis o ka maʻi. Inā mau nohoʻana i ineffective, hiki wale nō ke kōkua i ka i ka wā hoʻokahi transplantation o na maʻiʻaʻai a me ka naau. Transplantationʻoki kino o ke koa huikau, pono nui kālā koina. Ma ka kekahi lima, ka mea, 'aʻole e hoʻopau i ka pilikia o complications. I ka wā i nā pāʻoihana,ʻo nā nīnau mea straightforward, papalua transplant ke hoola i ka ola. Prior i kona manaʻo mea pono i kekahi, i ka luna '' inikua ninaninau.
Pehea e hoʻomanawanui iki mai me Eisenmenger maʻi pale?
Kanaka, ka poe i, e hana me keia cardiac maʻi, pinepine i kaʻeleu ola. Naʻe, ka mea, i ke mau e hele i ke kauka, a ke kanaka hoʻoponopono ola nā hoailona. Oia nā mea maʻi e pale aku dehydration, hooloihi ae i waiū e kiʻekiʻena infectious maʻi. He nui, e haawi aku iʻinoʻano a me ka lawe lapaʻauʻia i hiki i kahe ana ke koko. Inā ka hoʻomanawanui penei kauka mau kauoha, i ka pahiki o ka manawa kūpono e alakai i ka maʻamau ola, piʻi pū. I ole ia, ke koko oxygen ma kaʻilikai i haule i ka noho pilikia pae i alakai i ka make.
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