Ola kino, Maʻi a me nā kūlana
Kailua ka maʻi - i hūnāʻia pilikia o
Lapaʻau pili puke haawi aku i ka loa luna 'ka wehewehena o ka maʻi, i ua kapaia o Kailua i ka maʻi. I mea e maopopo i nā kêia kanaka a me nā 'ano o keia maʻi weliweli, ia mea e pono ai maopopo i mua i kēlā me kēia kau ua hoʻohana' ia i loko o kona ho'ākāka 'ana.
I ka maʻi ua manaoia e e hereditary, autosomal Hoʻohaku. Kēia 'o ia hoʻi i ka maʻi, ua aaiaoe, a ili mai kekahi makua, e halihali i ka liʻiliʻi loa hoʻokahi mutated'ōewe. Ka mea hiki wale mai i waena o nā keiki kāne a me nā kaikamāhine'ālike.
Kailua ka maʻi - he maʻi o ka maʻi e holumua ai. Ua UaʻAʻoleʻia, ka mea e hoʻomōhala ana i lohi, mau mahuahua symptoms, i kekahi manawa neʻe maila i loko o ka huʻi ke kahua. I ka maʻi ua mau pu ma ka noʻonoʻo 'kāna hana, extrapyramidal kāna hana (ana kāna hana).
Ke pathogenesis o keia kāna hana i ua? Anoee loa poorly. Naʻe, ka mea, ua ike ia i loko o kanaka e hoomanawanui i ka pinepine he shortage o Gaba (aminobutyricʻakika, i mea no ka mea nui inhibitory neurotransmitter) i loko o ka lolo keena. Ia manawa, ma na keena o ka substantia nigra ana maoli i ke dala o ka hao, he meaʻoi kāna hana o ka dopamine pūnao. Kekahi poe akamai i manaoio i ka maʻi Kailua ka maʻi ua kena ae la ia e hooloihiia mai kaulahao o ka'amino nāʻakika. Nolaila synthesized "hewa" kumuʻiʻo hōʻoni i ka biochemical keʻano o ka hanaʻana i loko o ka lolo.
He mea maopopo loa hoʻokumu i ka pahiki o ka ke keiki me ka maʻi i loko o ka ohana Media poino'ōewe mea 1: 1 nānā 'ole o ka wahine o ke keiki.
Symptoms o Kailua ka chorea
Kailua ka maʻi nō kāu i kekahi 'i 30 makahiki (i kekahi manawa hope). Mua, ma laila nō ka 'imi naʻauao kāna hana: he hou o ka ike paka i, "Jam" ma kekahi manaʻo. People lilo aku i ka hiki ke kālailai i kiekie, a hoʻoholo i ka hopena.
Ua mau kāna hana i loko o hoʻomōhala holomua dementia. Ke hoomanawanui hoʻomaka koke depleted manao, i ka intellect degrades nalo ka hoao ana. Ua hoohaahaaia iho kanaka o ka hoʻomanawanui.
Ma ia laua, ulu hyperkinetic kāna hana. Hoʻomanawanui iki mai i kaʻike, o "Kailua ka maʻi" involuntarily ka hoʻomakaʻana e hana i ka hailona no ka poe liilii, neʻe, pela losing i ka hiki i ka paka na mea hana. No ka laʻana, e hele pū ana laila, e hooluhi ana i na lima a me ka m. P.
Kailua ka maʻi nei i ka ia. I kekahi manawa, ka oi aku ma ke kakahiaka nui kahua o ka hoʻonaʻauao, nā mea maʻi e willpower e uhi ai i ka ikaika hyperkinesis, a me nā hihia ka mea, hiki ke kaheaia loa poorly. Dementia maʻi ua mau pu, akā, i ka degere o kona oolea i e okoa. I kekahi manawa nā mea maʻi, ma naʻe o ka incessant hoʻololi iho, e malama i ko lakou Kora naʻEsau iho, a me kekahi manawa lilo ia loa koke. He aha hoike no ia mau hiʻona, ka lapaʻau ua ole i hookupaaia.
Kailua ka maʻi. ʻike, a me ka lapaʻau
No kaʻike,, e hoomanawanui i pono undergo EEG, MRI. IeAUPIIe, IAa IO i heluʻia kēia mau haʻawina atrophy o ka cerebral cortex, a me ka loli i loko o kona uila haʻawina, loaʻa mea he ai-kapaia indentation a me ka thalamus.
No ka hoakaka o ka meaʻike,, i hookolokolo aku la ia kauka i ka cerebrospinal loli, këia i ka mōʻaukala o ka maʻi i loko o ka 'ohana. I kēia lā hou, a hou aku i mahele hana no preclinicalʻike, no kaʻohana a pau e noho ana ma ke kamepiula pae. , Ae waiho nei i loko o ka pā lonoaʻili o lymphocytes e noiʻi i X-kukuna. Keiki hānau i loko o nāʻohana a pau he mea he maʻi lawe, e ia i loko o ka 'inikua moʻolelo.
Kailua ka maʻi, he maʻi. I mea e kōkua ai i ka hoʻomanawanui i ka ke ano hiki ke hāʻawi i ka pono a pau o ka triftazine, reserpine a me nā dopamine hakaka a me tranquilizers.
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