Mauriac maʻi pale ma ka mimikō

Mauriac maʻi pale - he maʻi e hoʻomōhala ana i like me ka complication ku i kūpono lapaʻau o mimikō ma ka manawa'ōpio wale nō. No ka mea manawa mua i hōʻike i ka maʻi i loko o 1930 ma Farani kauka Pierre Mauriac kumu. He hōʻike i ke ano o ka lapaʻau kiʻi i loko o i na keiki e loaa ana mai ka mimikō a me ka insulina Inc hala ka hewa laʻau heluna, hana kekahi mawaho hoailona. He i kekahi mea o nā keiki a pau i like i ka nānā aku, a ua lewa i loko o ka haʻahaʻa ulu, obesity, retarded moe ulu.

Nā kumu o ka maʻi

I ka papa kuhikuhiE kumu o ka loa complications mea pololei ole hahai aku la i mimikō Inc. Ma keia maʻi ka pancreas ua ole ke hoʻohana pono,ʻaʻole hua lawa mea o ka insulina. Aie i ka pathology ia lŘlŘ monakō koko deficiency i loko o na keena aie i ka mea i ka mea noʻonoʻo ma ka nui dala i loko o ke koko.

Mauriac maʻi pale 'ana i loko o nā mea maʻi me ka mimikō mellitus type 1 ua pili me ka lawa ponoʻole lapaau. Maʻi keiki no ka lōʻihi manawa lawa insulina mahele lāʻau lawelawe, a hoʻohana 'ia nā huahana o haʻahaʻa ka pono a me ka hewa maloko, e alakai ana i ka maʻi deficiency o insulina.

Hooloihi ae i ka nele o ka insulina i loko o ke kino,ʻo ia ka mea i kēia keʻano o ka hanaʻana.

• Metabolic kāna hana, pakahi aku la ia i ka kāna hana o ka carbohydrate pūnao.
• Mahuahua i ka nui o ke ake, a kona momoma degeneration ma muli o ka mahuahua glycogen hālāwai hope.
• Loli i loko o ke koko, haku mele 'ana - mahuahua i loko o ke koko monakō koko, naʻokoko, momoma nāʻakika.

Inā keia mea ole a pau pathological keʻano o ka hanaʻana i loko o ke kino i Mauriac maʻi pale, i pediatric hoʻomanawanui iki mai ka mahina i ka penei deviations:

• Lawa? Iecaianoaaiiuo o ka nui hormones - cortisol, ulu hōmona, glucagon, a like me kaʻilihune o ka 'aʻe' ana i ka ulu kaʻina.
• Hālāwai hope o nā polokina a me ka waiwai ia auoiaea kalipuna a me ka phosphorus mai iwi, e ho'ōla e alakai ana i ka hooulu ana o ka osteoporosis a me kekahi Muscle atrophy.
• Hikiʻole omo o nā wikamina i loko o ka naʻau liʻiliʻi.

Ka maʻi ana hoike mai ai ia ia iho, ma waena o nā makahiki o 15-18 makahiki, akā, i ka dysfunctional kaʻina hoʻomaka nui mamua. I kēia manawa, no ka iapaau ana o kakahiaka diabetic hoʻohana kēia a me ka pono hoomaemaeia hoomakaukau, aʻaneʻane eliminates ka hooulu ana o Mauriac maʻi pale.

symptomatology o ka maʻi

Mauriac maʻi pale mimikō i ka helu o nā mea hoʻomaoe.

• Ke keiki lagging hope ma ka ulu a me ka ulu ana o ka inhibition. Pinepine he mea obesity a me ka pōkole ke kino o Iesu. Ma keia hihia, he maʻi keiki ke lag ma hope o kā lākou mau na¯ i loko o ka ulu ana ma 10-30 kenimika.
• Ke lag ma ka moe? Acaeoey (underdeveloped moe 'ano a me ka wa e kaawale aku o ka menstruation i kaikamahine).
• Protracted puberty.
• Obesity, ka oi aku i loko o ka maka a me ka hoaka o ke kino me ka lahilahi lala. Maʻi keiki i mea i like loa, i ka "crescent-hoʻokino" ma kēlā me ka maka, pōkole'ā'ī, momona i loko o nā lima, poohiwi, abdomen. I ka haʻahaʻa o ke kino ka loa lahilahi.
• Hoomahuahua ae la lakou ake pu aku huakaʻi venous holo.
• Osteoporosis (ka meheu o ia i ka hooulu ana o ka iwi'aʻaʻa).
• maka maʻi, a me nā maʻi o ka retina, a a laila i ka ulu ana o cataracts.

Ka loa, he pono ole Mauriac maʻi pale i na keiki, i ka maʻi keiki Hawaii photo hōʻike i symptoms i ka maʻi.

ʻike, no ka maʻi

I kaʻike, o "Mauriac maʻi pale" ua hoonoho i ke ahuwale mawaho hoailona o ka maʻi, e like me: ka nele o ke kiekie no ka makahiki, i ke alo o ka obesity, o ka oi aku i loko o ka maka o ka moe immaturity, he ike ulu i loko o ke akepaʻa.

E hoʻokūpaʻa i kaʻike, lawe mai ke koko o Kaoleioku, i kūpono i ka mea kēia mau hoikeana i:

• lolelua ka monakō koko pae, e hōʻike ikaika Lele i loko o ka nui, a laila, iho.
• Excessive koko lipids (hyperlipidemia).
• A nui mahuahua ana i loko o ke koko naʻokoko pae (hypercholesterolemia).

Ma kekahi mau hihia, hou hoʻopaʻa haʻawina ake biopsy no keia mea, e lawe mai i ka momona haawe

i ka maʻi

No ka'ōpio kino i ka maʻi mea paʻakikī loa. E like me ka nui 'ano o nā mimikō, ia mea paakiki ke compensate no. Pinepine ke kumu no acidosis a me hyperglycemic coma.

Mauriac maʻi pale ia lŘlŘ ma ka loa, no ka mea o pinepine hou o kela infectious maʻi, like hoʻi me eiiieaena, a lengthy ke ola biochemical keʻano o ka hanaʻana i loko o ke kino.

Mauriac maʻi pale a me Nobekura: like a me nń

Mauriac maʻi pale a me Nobekura pinepine e hoʻomōhala ana i ka noho 'ana kamaliʻi, nā maʻi nō he complication nui o ka mimikō e ia lŘlŘ ma luna o ke kāʻei kua o kūpono lapaau. He mau syndromes i like symptoms, e nā ulu retardation a me ka moe? Acaeoey, he protracted adolescence, momoma akepaʻa. Ma keia hihia, me kaʻole o Nobekura maʻi pale o ka nele o ka oi kino momona. Ma keia hihia, no ka iapaau ana o nā syndromes AIM e eha i ka iapaau ana o mimikō.

Mauriac maʻi pale lapaʻau

Direct lapaau o ka maʻi pale me keia hakuʻole. All Inc nona ma kamaʻilio akula i ke kumu kumu o ka maʻi a me ka complications, kena ae la ia e ia. E hana i kēia, i ka hoʻomanawanui ua häʻawi mai ai i ka pololei insulina Inc ma ka pololei a me ka laʻau heluna kona mea e like me kaʻiʻo nō o kēia ai '.

E ole lipodystrophy paa iho la i ka helu o ke kāohi kaʻina hana no kēia mea i'ōleloʻia ai e like me ka lomilomi, physiotherapy a me nńnń no insulina injections. kūikawāʻai hiki ke hāʻawi ma ka hou i ka lapaʻau, e hoʻokoe 'ia mai i kaʻai a pauʻai i loaʻa ka holoholona bipi kūpaluʻia. Ma keia hihia, no kaʻai e kālele ana ma luna o kumuʻiʻo a me ka carbohydrateʻai.

Lapaʻau Inc ua kekahi papahana e compensate hoʻomōhala ma ke kāʻei kua o ka nń ku maʻi complications no kēia ahonui naznachetsya:

• Komo gepatoprotektorov e hoʻihoʻi ake keena.
• B nā wikamina e hoihoi maʻamau pūnao.
• Complex lāʻau nona ma normalizing i ka pae ana o lipids a me ka naʻokoko i loko o ke koko.
• Steroid ai 'e kāhea ulu i ke kino o ka.
• Hormonal ai 'e hoihoi nui' īnea i hana.

Kāohiʻana a me ka prognosis

E pale aku i kēia mea pepehi complication o mimikō like Mauriac maʻi pale, ia mea e pono ke lawe mai i ka pololei lapaau o ka nń ku maʻi a me ka pale insulina deficiency.

I ka hui lapaʻau i mua ulu ka maʻi pale laekahi 'ai' prognosis maikaʻi lawa, akā, inā pau ka kauka mau koi. e hiki ke hoʻi i ke keiki ka ola, o ka poe mawaho, a na ka pololei laʻau heluna o ka insulina, a hoʻihoʻi hou functionality o nā mea a pau nā loko iʻa.