Ola kino, Maʻi a me nā kūlana
Rasmussen ka maʻi (encephalitis). Kumu Rasmussen maʻi pale
Rasmussen ka maʻi pili i ka waeʻano o pohihihi keia hoʻoʻino mai e poha mai i loko o ka lolo. Kēia encephalitis ana ia lŘlŘ i na keiki ma lalo o 15 makahiki. Loa pinepine, i ka maʻi ua diagnosed ma Nalani Olds. Ma adolescents a me nā mākua, i kēiaʻano o ka encephalitis ka loa pohihihi keia.
Ke kaʻina komo ai kekahi 'ole ka' ē aʻe hemisphere o ka lolo. E like me ka maʻi progresses, kauka ike ia e holumua ai atrophy. Kauka kuhikuhi ana i ka lōʻihi ia'ku i ka maʻi kūlana kanaka. I mea, o ka Rasmussen maʻi - encephalitis me ka ho'ākāka 'ia i nā hiʻona i hiki ole ke ola.
Paha kumu encephalitis Rasmussen
Up a ka etiology o ka maʻi i ole, ua hoʻokumu. Epekema wale hōʻike 'ekolu ki aʻe i hiki hoʻomaka, a mālama aku i ka Holomua o ka pathological ana i kupu mai ma ka Central ko mākou hopohopo nenoaiu. A iiiaanoaa o ka lapaau manaoio i Rasmussen maʻi pale ua kena ae la ia e autoimmune nā mea'aʻaʻa, nā mea hoʻomaʻi a me ka cytotoxic T-lymphocytes.
Hiki kūlana o ka cytomegalovirus, i i kaʻawale mai ka cerebral cortex o kanaka makua nā mea maʻi. He hiki i kēia mau pathogens i li nui, ulu i loko o ka maʻi maʻi. Eia hou, ka mea hiki ke precipitated complicationsʻikeʻia ma hope mamua maʻiʻaʻai.
Ano, ka hapanui o nä känaka 'epekema manaoio ana ia mea he autoimmune nā mea'aʻaʻa pono encephalitis Rasmussen. Nā kumu o ka maʻi ua i manaoio aku ia e wehewehe e cytotoxic T-lymphocytes.
Ma nā mea maʻi me Rasmussen ka maʻi pale, i kekahi manawa, i loaʻa i waena o poe hoahanau, ka poe e ae, mai autoimmune maʻi 'ē aʻe. No ka laʻana, Behçet ka maʻi. Kēia paipai i ke kuhiakau i hoahanau i komo i loko o ka pathological kaʻina, he pono ole aaiaoe, ao ke ano. Ma kekahi, e haawiia keia i kumumea like me HLA-galotipy.
Symptomatology entsifalita Rasmussen
Initially, ka maʻi hoike mai ai ia mea nui Hawaii ke kāʻili 'ana. E like me ka maʻi ino e hui kūloko myoclonus. Over manawa, me ka ho'āhewa waleʻoi loa. Ka mea, i hele pu me ia e Muscle spasms, poho o ka ike paka i a me ka hina. Pinepine, i ke ehuehu o nā mea maʻi me ka ho'āhewa wale i ka hiamoe.
I holopono nō, ka maʻi hoike mai ai ia ia iho, poho o ka ikaika a me ka hapa numbness 'ia i loko o kekahi hapa o ke kino. Haʻawina hōʻike he emi ma ka ha awina ma ka hoʻohuli ai i nā lolo wahi.
lapaʻau '
Symptoms haʻi i kanaka e loaa ana i ka makahiki, a me ka maʻi pale o Rasmussen. Encephalitis me ka etiology o ka ho'āʻo e hōʻike i kakahiaka nui me hiki. Kēia e leie aku iā mākou i ka manaolana no ka maikaʻi loa o immunosuppressive Inc. A mua o nā mea a pau io i ke ao o ka lapaʻau, MRI a me EEG ua hana.
Nā Papahana O Ka lapaʻau o Rasmussen ka encephalitis
No ka mea, no laila, hiki, aia no na hoopaapaa e pili ana i na kumu o ko Rasmussen ka maʻi pale, encephalitisʻaʻole ia eʻike mau ki ina hana like. Inā kakahiaka ka loaʻaʻana o ka maʻi i hoakaka ia antiepileptic lapaʻauʻia külana. Paipai aku i kaʻai ke hoʻololi, e hoomahuahua i ka hoopau ana o kaʻai waiwai ma ka kaikea, a me ka ka ho'ēmiʻana i loko o ka nui o kaʻaiʻai i loaʻa carbohydrates. Pinepine i loaʻa ka mea pono e hana plasmapheresis, corticosteroids, immunoglobulins.
Pinepine, i ka lapaau ana i ka maʻi i akoakoaia i'ano'ē ki ina hana like. E hoomanawanui i ka poe i loaa ia i ka maʻi nui a me ka luna 'lolo poino, ia mea pono e hana transplants o nā aʻalolo keena. Ano, a hiki i hiki mākou ho'āʻo mai i ka hoʻomaka craniotomy.
I kekahi manawa, e hoomanawanui i mohai akuʻoki lāʻau lapaʻau 'uao - Hemispherectomy. Ma hope o ka mea hiki e Rasmussen ka maʻi pale. Encephalitis, o ka papa, na lau kona ko läkou ', hai paresis a pilikia me ka olelo. Naʻe, pepehi i ka hoʻomanawanui i emi, he pono ole.
E haawi aku iʻoki kino mea i kupono, hoʻowahāwahā i ka mea i ka mea, aole ia i alakai i ka hoʻokō 'ia e olaʻi. Ma hope o nā mea a pau, i ke kūpono 'ana o ka maʻi aggravates paakiki neurological nele, e ku e ia a loaʻa nō noʻonoʻo retardation a me ka lōlō.
Ma na hihia aʻeluaʻaoʻao lesions o ka lolo (nā hemispheres) i ka olelo wanana Eia naʻe noho lakou malaila. Hihia o ka make i waena o nā mea maʻi me ka encephalitis Rasmussen Aloha ole uncommon.
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