Sideroblastic anaemia: symptoms, lapaʻau

He nui nā poʻeʻike i anaemia mea he mea weliweli loa maʻi. Ua nuiʻano likeʻole o kēia maʻi, a me ka mea palapala i kanaka ola kēlā me kēia no ia. Sideroblastic anaemia mea he mea pepehi pathology hou pili i ka hihia hoʻi microelements hoʻololi kemikala. Ma keia maʻi i ka iwi lolo ma ka hao no ka hemoglobin 'ē aʻe, no laila, ka mea, ua waihoia ma na nā loko. Na ka papa kuhikuhiE mea - e pale aku complications, a no keia kumu e e koke imi 'oihana kōkua.

manaʻo

Sideroblastic anaemia i kekahi, mai nā 'ano o ka maʻi hoemi lehulehu o ka hao i loko o ka ula keena. Ka mea i ka iwi lolo aole e hoʻohana i kēia hehee ai i loko o ka hoʻololi kemikala o hemoglobin. Loa pinepine, i ka maʻi e hoʻomōhala ana i like congenital a loaa. Ma ka aaiaoe iliwai, anaemia ia lŘlŘ ka hapanui i loko o nā keikikāne.

Ka maʻi hiki ke pū i hiki i ka autosomal Hoʻohaku ala. Keia ua kapa anaemia maʻi pale Pearson. A hiki aku i ke kino ua poorly paka hao, ka mea, ua waihoia ma na nā loko, kūpono ma sideroblastic anaemia. Inā ka gland lilo nui loa, i ka hana a ua wāwahi ake, hakuʻala a me ka naau Muscle.

'ano o ka maʻi

Kēiaʻano o ka anaemia ua puunaueia ma ke degere o ka oolea, akā, no hoi, no ka ka helehelena, a me ka lapaʻau kiʻi. Kekahi mau okoa ano o sideroblastic anaemia:

1. Hereditary. I ka maʻi ua ili like me ka hopena o ka'ōewe mutation. He kumu no ka anomaly pathology metabolic aʻee komo nei wikamina B6 a me ka aminolevulinicʻakika. I ka maʻi i ia iho, i manao ai ma hope o ka hānau 'ole adolescence oiai.
2. Congenital. Kēia palapala Ua kaʻawale kaawale,ʻoiai i loko o kekahi mau loa ka mea pili i ka hereditary ano. Here, wehewehe aku ma ka maʻiʻo kiʻekiʻe o erythrocyte coproporphyrin.
3. Loaa ana. Eia kahi mea akaka i ka hopena o ka adverse hopena o Nine Inch. Iwaena o lakou i ethanol, kēpau, tsiklosirin.

Pilikia me ka hao hoʻololi kemikala i hoʻomaka ai ma muli o keʻeho keʻano o ka hanaʻana i loko o ke kino. Kahi o 1/10 o nā mea maʻi me ka sideroblastic anaemia poino mai ka huʻi leukemia.

Kumu o ka maʻi

Ke iniiaiie kumu o ka maʻi o ka nele protoporfiirina, i mea kekahi o ka loa nui eiiiiiaiou o ka hoʻololi kemikala o hemoglobin hehee ai. Eia hou kekahi, 'ona' ole ma o ka hana ana o ka hou kumuʻiʻo a me ka hao.

Lilo palapala sideroblastic anaemia kupu mai ka mea i ke kino, aole ia e komo i ka mea 'ona i loko o ke kupono nui. Aia mau wahi, i hiki ai i ka makemake hui i uhi pū me ka laau i lawe kanaka.

Ke kino ua depleted like me ka hopena o ka waiū i ka waiʻona. Anemia kānāwai ma muli o ke alakai i kaʻapu kōheoheo a? Eaia o antibiotics ikaika. Ke hereditary palapala Ua hooholoia ma ka wahine chromosome poino genome. Nō hoʻi, i ke kumu o ka maʻi i ia i kāna hana o ka'ōnaehana paleʻea'ōnaehana a me ka hooulu ana o neoplastic keʻano o ka hanaʻana.

ʻike, sideroblastic anemia

Ke kaʻina o nä ka maʻi o loa eiiieaen, no ka mea, puka mai aneane asymptomatic. A, aia no he okoa lapaʻau kiʻi, a au hiki ke paulele. Inā 'oe e nana wale i ka mawaho hoailona, i kaʻike, o keia maʻi mea unreal. Eia naʻe, he mea kekahiʻaoʻao, e huai ae sideroblastic anaemia - he koko hōʻike.

Kekahi hana ka ninaninau ana i na nā loko o ka hoomanawanui, e imi i hao hoʻokomo kālā. Akā, ma ka manawa hehee ai, a no laila, ka mea e hookomo ana hematological symptoms. E pale hewa, ia mea pono e hōʻoia i kaʻike,. Keia ua hana ia me ke kōkua o kekahi macroscopic study o ka iwi lolo.

I mea i ke kamepiula ua minimized, ia mea pono e hoʻomaka i ka biopsy. He kēia kaʻina hana o ka loa ka hoʻokō ala e hooholo sideroblastic anaemia. Ua Ua lawe mai like penei: mālama '-hoʻohaumiaʻo biopsy kūikawā waiwai, a ina i ka' akomi i ole-synthesized hao, 'elele i huiʻia e hiki.

I ka mea akamai i ka hoʻoponopono 'ana i?

I ua kaulana, ka symptoms o ka anaemia sideroblastic kokoke manaʻo. Ka lapaʻau kiʻi Ua i nalowale, a no ka mea, aia nō kekahi mau pilikia. Inā he kanaka Kahalaopuna luhi, nawaliwali ma ke kino, ka mea i hookuu pili i ke kino. A kauka no kēia anaemia aku ai ke hoʻomanawanui i ka hematologist i ke alakaʻi i ke ana manaʻo.

Mua, i ke akamai loaʻa mau moku'āina o ka hoʻomanawanui ka hoihoi i loko o Hawaii, inoʻano, he papa inoa o ka maʻi, aʻula a 'ole, D. Inā ke kahuna lapaau deems pono ai,ʻo ia, e hoopaa mau haʻawina. Mau nā:

• koko (a biochemical);
• ake biopsy;
• Ka Ikepili o ka iwi lolo aeea haku mele 'ana.

Hematologist ke kohoʻia kauoha i ka hoʻomanawanui i nā hoʻomalu no ka oi piha ninaninau. No ka laʻana, e imi i ke ano o ka anaemia, ia mea pono e huli i ka aaiaoe?. Keia kauka e ike ai i ko he mea ia e ka hereditary ano o sideroblastic anaemia. Ua hiki no hoi e pono ai, e nīnau aku i ka gynecologist, urologist paha proctologist.

Nā Papahana O Ka lapaʻau

Mua oe hoʻomaka lapaʻau, e pono e ike ai i ko laila mea, he hao palapala moʻopane. No keia mea, desferalovuyu hāpana. Ua Ua lawelawe ma intramuscular ka pahu kui, a me ke kūpono mimi E e anao? Aou ka hola 0.5-1.1 mg o ka hao, a ma hypochromic, gipersideremicheskoy, sideroahrestical, sideroblastic anaemia - 5,10 mg.

He waiwai 'ana i kumumanaʻo,ʻaʻole e i ka hereditary ano o ka maʻi ke ola. E uhi'ōewe a hoomaka ae la e mutate pinepine hoʻohana lapaʻau me kiʻekiʻe nā māhele o ka wikamina B6. Ua Ua lawelawe i loko o ka nui o ka 100 mg no ka lā. Naʻe, i ka naoh o ke kino, ua kokoke unpredictable. Ma ka iapaau ana o sideroblastic anaemia hemoglobin pae e ku i ka mahana maʻamau i loko o na malama ekolu. Inā i keia wā o ka manawa, aole ia i ke kōkua, hou lapuwale Inc.

Kāohiʻana a me ka prognosis

Muli o kona kulana pinepine, i ka maʻi ia lŘlŘ like me ka hopena o ke alakaʻi i kaʻapu kōheoheo. E pale aku i kēia, pono e lawe malama, e hana i kēia mea. Iloko o ke? Aeiino? O kahiko hale e pono ai, e lawe kaiapuni i hiki i ka manawa resettle keiki. Mai hoolilo o ka paha kanu HW i loaʻa kēpau. He aho e kepa ai a lawe ia chemically. Eia hou, i ka pono, e mau kanaka hoʻoponopono i ka Hoʻomaʻemaʻe o ka pa, like me ka hale a me ka ola hae.

Hoola i ka hereditary ano o ka maʻi he mea hiki ole. I mea e hoʻopaʻa ai i ka pono 'ole pono e mau kanaka hoʻoponopono i ka helu koko, oi loa ka nui o ka hemoglobin. Keia ua loaʻa ma ka pololei, e hooholo ia ana o ka papa o ka Inc, a 'aʻole i' ae i ka maʻi, e hoʻomohala a malama i ka maʻamau ke ano o ke kanaka.