Ola kino, Maʻi a me nā kūlana
Hahai mai: Symptoms a me ka lapaʻau Nā Papahana
Epidermolysis bullosa, a me ka maʻi hahai - he maʻi pohihihi a me ka weliweli. Kēia aaiaoe ano o ka dermatitis, a ua wehewehe aku ma congenital mā i loko o ka 'ole o ka ili. Eia naʻe, i ka lā,ʻaʻole nō he pono ka hana o ia kāna hana.
Hahai mai: mea, lalau mai a me symptoms. E like me ua oleloia, e like me ka maʻi mea hereditary, a akaka, me he rula, koke ma hope o ka hanau ana. No ke aha lā i kēia maʻi? Mua mākou Pono e noonoo i ka 'ole o ka mea maʻamau kanaka ili.
Ma kānaka, i ka luna, ahu iho o ka ili a me epidermis, ua manaoia e hoomalu aku i ka hopena o ke kaiapuni. He ua maʻamau i pili i kaʻoi poepoe - na dermis. Hoʻomanawanui iki mai i kaʻike, o ka "maʻi hahai" pili ma waena o nā epidermis a me dermis e nalowale 'ole mea i ikaika loa, e hoopaa i na papa o ka ili a pau. Ia mea ke kumu o ka ili o ia i kekahi keiki, ua waihoia i ka hewa.
Epidermolysis bullosa ua hoike koke ma hope o ka hanau ana. Eia kahi mea akaka ma ka ili mai hehe, a ulcers a hiki i ka iki mawaho keiki. Inā he keiki hele mai i kekahi mea, a laila, ma luna o kaʻili e ike koke ia. O ka holo ana, me ka hahai i ka maʻi ua pu e mau eha.
E like me ka maʻi no hoi e loli ai i ka mucous membranes o nā maka, waha, larynx, no ka i ka mea i pono, e hānai i ke keiki. Ma ka hopeʻanuʻu hiki e malama niho poho, poho esophageal mucosa a me ka naʻau liʻiliʻi.
O ka holo ana, i ka maʻi iho mea ole ona e hahai. Akā, e noho i loko o kēia moku'āina mea pilikia. Eia hou kekahi, paʻa eha, poorly ka hoola ana i na mai hehe, a blisters i maikai'īpuka i ka fungal, mea koʻohune a me ka mea hoʻomaʻi nā mea palahēhē. I ka wa e kaawale aku o ka mea kupono malama sepsis ulu ua mālama a me ka helehelena o ka foci o necrosis.
Epidermolysis bullosa: kūlana kanaka. Eia naʻe, i ka maʻi mea maʻi hiki i keia la. I ka papa kuhikuhiE kūlana kanaka i manao e pale maʻiʻaʻai a me ka sepsis ulu.
Ma kekahi mau hihia, nele i ke keiki regular Inc me glucocorticoids. Oia lapaau kōkua pale aku i ke ano o ka poʻe noʻonoʻoʻole, a blisters ma luna o kaʻili, mucous membranes, na nā loko. I kekahi manawa, lawe mai a me ka lapaʻau me immunomodulators, i kōkua i ke kino kaua nā mea palahēhē.
Pono ka A maʻi keiki a eia i malama, i ka loaʻa o ka pololei, disinfection o ka eha a me ka dressings. Eha ia me kaʻoliva kaʻaila, nā wikamina, pāʻoihana, me ka hinu a me antibiotics maʻiʻo, infusions o ka lāʻau lapaʻau lau nahele. Loa pono no ka mea hoʻomanawanui ili o ka pākōlea auau me ka decoction o ka lāʻauʻoka wauke, succession, chamomile a he nawaliwali pāʻoihana o ke potasiuma permanganate.
E e uku ia mau noonoo i kaʻai. Ma ka mahina mua o ke ola, umauma-e ai ana, ua pono. A laila i ka ai e e loli, me ka paakai, na mea ala, a me kekahi o keʻano ukiuki huahana. Ma hope o, e ai ana, e holoiʻia ia i ke keiki i kou waha me ka mehana, hōʻuluʻulu manaʻo me ka wai - keia mea e pale aku i ka muli o Oe, a festering ma ka nui aʻe ana.
Shoes a me ka aahu e e like palupalu, a i wale nō, mai maoli fabrics. Inā na iwi i i ino, ua i ke keiki, e hoʻoneʻe - keia, e kōkua pale aku i keʻano o nā contractures.
I ka maʻi ua pinepine pu ma ka hooulu ana o ka hahai anaemia, i mea loa pilikia no ka maʻi keiki. He nolaila, e pono ai ka mea ana ka mālamaʻana o ke koko kūlana haʻahaʻa, a ina e pono ai - ka transfusion o ka wai koko a me ka albumin.
I kekahi manawa, hoʻohana 'ia i loko o ka iapaau ana o "Tocopherol'ākeka" - he lāʻau e stimulates ka? Iecaianoaaiiie o laholio a me ka collagen olona, o na dermis. Inc i wahi i loko o kekahi mau kahua o ka hoʻonaʻauao, a me ka loaʻa o kekahi mau puana papa. No kekahi nā mea maʻi, ia mea ua lilo ke ola i kēia lapaau.
Ma kekahi hihia, i ka maʻi hahai - mea nui maʻi i ka pono a eia i lapaau.
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