Ola kino, Maʻi a me nā kūlana
Aplastic anaemia: symptoms. ʻike, a me ka lapaʻau o ka anemia aplastic
Kēia manawa, aia nō he wahi lihi iki o keʻano o ka maʻi i i ua hoʻopili 'ana i ke koko. Kekahi o kēia mau mea aplastic anaemia. Nā symptoms o keia maʻi hōʻike,ʻaʻole i kekahi manawa. Ua mea hiki e hoola i ka maʻi? He aha nō ke kāohi ana? A no ka mea, a ia e komo i loko o kēia 'atikala.
Overview
Aplastic anaemia mea he maʻi o ka hematopoietic'ōnaehana, ma he mea iʻoi emi i loko o ka helu o ke koko keena, akā,ʻaʻohe overt na hoailona o ka maʻi 'aʻai. E like me ka poe akamai, keia pathology mea pohihihi keia. Hiki ke hana ino i nā kānaka, a me ka nani ke keka, IeAUPIIe, IAa IO ma hope o 50 makahiki. I ka haʻalele untreated anaemia aplastic mea pinepine ona.
maomeka o ka maʻi ulu
Ua ua ike ia i ke kahua o ke koko ua lawe mai ma ka kūikawā pūʻulu o aeee, oia hoi hematopoietic anei i keena. Ka mea, i ka hiki e proliferate a differentiate i loko o kekahiʻano o ke kupu ma ka hopena hematopoiesis. Ua mea no ka mea, o ka mea hope i hana oo aeee (erythrocytes, leukocytes, platelets, etc.). Ma lalo o ka aoao o ka helu ana mawaho a me na aʻe, ke kēia sequential kūpono 'ana o ka maʻi maomeka:
- ke kiʻekiʻe o ka hōʻemiʻana i ka nui o hematopoietic anei i keena;
- pilikia iniiaiie hana o ka anei i aeee i entail ka impossibility o ke kahua o erythrocytes, thrombocytes a me leukocytes;
Make anei i aeea ma keia hihia hōʻoia ana i ka laulā o ka iwi lolo transplantation mai'ālike mahoe a kaikaina / kaikuwahine. Ua ua malamaia lakou nei, pela anaemia aplastic i loko o nā keiki a me nā mākua. Eia naʻe, transplantation mea i mana, mai ka 'ālike māhoe i loko o ka hanana i ka haumāna haʻawina kālā i loaa i mālama '-papa o ka ai', e uhi i ka'ōnaehana paleʻea nenoaiu. Keia mea ua loa pinepine hoʻopaʻa i ka'ōnaehana paleʻea ano o ka maʻi.
Ke kumu nui
Eia naʻe, i ka etiological kumumea o ka maʻi i ike ole ia a hiki i ka hopena. manaʻo akamai i ke kumu i e:
- regular hui 'ana me kekahi pūʻulu o Nine Inch;
- waiʻona hainā;
- aaiaoe predisposition;
- ionizing pāhawewe;
- intoxication ai ';
- kekahi infectious maʻi;
Inā poe akamai i hiki ole kukulu iho la lakou i ka pololei loulou me na kumu i haiia ae maluna, ua kapaʻia ka maʻi idiopathic anaemia aplastic.
symptoms
- Pale ili, i pēpē.
- Pokole o ka hanu.
- Mahuahua kino ana wela.
- Nawaliwali, luhi, pōniuniu.
- Tachycardia.
- Ulcerative stomatitis.
- Nasal a gingival kahe ana ke koko.
- Loss o ka ikaika loa ka makemake, ulia kaumaha me keia poho.
Kēia mea,ʻaʻole i ka lapaʻau hoailona like i ikea anaemia aplastic. Nā symptoms oiaio oko i loko o kēlā me kēia hihia. Eia hoʻi, ka mea pinepine e hoohalike ai nā maʻi 'ē aʻe o ka hematopoietic nenoaiu. Ia mea ke kumu ia mea nui e koke imi 'inikua noonoo, a, e haawi i na mea e ho'āʻo ai. Aia i kekahi mau rula o ke koko no kela a me keia keka a me ka makahiki. Inā, no ka laʻana, biochemistry nā hoailona e e iki okoa, ke kauka i mua i hoakaka ia oi piha hookolokolo, a laila, i ka hana kūpono.
shape
Hoʻomalu conditionally classify i ka maʻi kumu i loko o nā 'ano:
1.Vrozhdennaya aplastic anemia mea:
- hereditary (kahe o ke koko a me ka ho okumu congenital anomalies) Fanconi anaemia;
- hereditary (poho hematopoiesis me congenital anomalies i loko o ka ulu ana o ka) anaemia Oestrich-Dameshek;
- ka helehelena ulaula aeea aplasia (ua hoʻemiʻulaʻula koko aeea helu);
2.Priobretennye anaemia aplastic i:
- me ka huina pau lesion o hematopoiesis;
- me ka'ōnaehana hoʻokoho pio o ka erythropoiesis;
Eia hou, i ka maʻi ua hoʻolaha e like me ke oolea:
- Ole-loa aplastic anaemia. A koko ho'āʻo hōʻike kiʻekiʻe pae o kekahi mau constituents, akā,ʻaʻole lawa ka e like me ke kūmau.
- Loa aplastic anemia. Underreporting o platelets a me granulocytes ritikulotsitov.
Ai kā hemorrhagic anaemia?
He He 'ano like' ano o ka anaemia, a ia lŘlŘ no i ka loa koko poho, e alakai ana i ka pahikaua emi ma hemoglobin i loko o ke koko, i ka ulu ana o ka ai-kapaia vascular insufficiency a me ka oxygen pololi. No ka maʻamau makua kanaka pilikia kupu i loko o ka hihia o ke koko lilo aku i ka buke o ka 500 ml.
Kēia pathology ana ia lŘlŘ ka wā i ectopic hāpai keiki, i ke koko a me akepaa maʻi, loa koko emi hope hewa aʻoki kino.
Ua mea noteworthy i ka hoʻomanawanui i loko e no kekahi mau lā i ole manao i ke ola ana o keia pilikia. Haʻi symptoms hou 2-3 lā ma hope o ke koko poho. Inā ka hoʻomanawanui e ole loaa akamai malama, Ua kiʻekiʻe loa pahiki o ka make.
A pilikia e like me anaemia, hemorrhagic treatable. Ke kauka pono mua hoʻopau i ka papa kuhikuhiE kumu o ke koko a me ka poho transfusion hana colloidal pāʻoihana.
lapaʻau '
Loa pinepine kēia ka maʻi ia lŘlŘ ma hope o ka ae, haawi o kālailai preventively. Ma anemia, hoemiiaʻulaʻula koko aeee i loko o ke koko, keʻokeʻo koko keena, a hemoglobin indices, a ESR pae dramatically māhuahua. He nui e hoailona oukou i ka degere o ka ho'ēmiʻana i loko o ka maʻiʻo o nā eiiiiiaiou e ĸokoĸa ana nä pane ma kela a me keia kanaka hihia.
E hoʻokūpaʻa i ka maʻi anaemia aplastic, he koko ho'āʻo nei i ka pau iaoia o kaʻike,. Ke kahuna lapaau e pono ana waihona he oi piha ninaninau o ka hoomanawanui, a me kēia mau:
- physical ninaninau (manao paa o ke ano o kaʻili, ke koko,, ke alo o ka hemorrhage, a pela aku ...);
- mimi Ka Ikepili (alo aku o ke koko ua manaoia he hoailona ia o ka hemorrhagic maʻi pale, a me ke alo o microorganisms - ka hoike ana o ka infectious ano o complications);
- koko kemika (naʻokoko, monakō koko, uricʻakika);
- ke hoʻokō 'ia' inikua mōʻaukala (ina he mea inoʻano, ina paha he nui kekahi maʻi mai, ina paha o ka waiū i kaʻawahia waiwai);
- koko Ka Ikepili;
- like o ka iwi lolo puncture ano;
- electrocardiography;
He aha e e hana?
Mua o nā mea a pau ia e e kaulana ia wale palapala hōʻoia no hoʻokokoke ke kōkua nā mea maʻi i loko o ke kaua ana i ka maʻi e like me anemia aplastic. Symptoms o kēia maʻi i loko o ka kakahiaka kahua o ka hoʻonaʻauao e Alert a pau. ¶ A, i ka wa a ka iniiaiie lapaʻau na hoailona mea nui e koke imi 'inikua noonoo no ka mea e hooholo ia ana o piha ninaninau.
Hoikehonua, lapaau e kaumaha ana ekolu koho no ka Inc. Lalo o ka nana aku ma kēlā me kēia i loko o hou au mamuli.
- Causative lapaʻau ua waiho i loko o ka hihia i ike ia i anemia. Ma keia kulana, o ka pahuhopu nui o ka Inc mea, e olelo ana ma o ka hoonaukiuki ololi, akā, ia mea pinepine ineffective. Hoʻomanawanui iki mai i ka manao, e hoʻopau i ke kumu kumu o ka maʻi (wehe 'ia? Aie? Pāhawewe, ke kāpaeʻana o kekahi lapaʻauʻia, a pela aku .. D.). Oia ana emi wale i ka uku o ka make ana o ka iwi lolo, akā,ʻaʻole e hoʻihoʻi aku i ke koko maʻamau.
- Pathogenic lapaʻau hoʻohuʻu he ulu ke kāpaeʻana maʻi maomeka. No kēia mau mea, hoʻohana immunosuppressive Inc ( "Cyclophosphamide" ai ', "Cyclosporin"). Ma kekahi mau hihia, i ka hoʻohana i kēia mau ai 'hiki hematopoietic kuleana pili i loa e hoihoi. Ua ua i hoʻohana 'ia i loko o ka lapaau ana o corticosteroids a me ka lāʻau anabolic steroid i. Mau laau e ole hoʻoulu wale i ka? Iecaianoaaiiie o keʻokeʻo koko keena, akā, i ka hōʻoi 'kumuʻiʻo hoʻololi kemikala. I loa ano o ka maʻi, kauka waiho aku i ka iwi lolo transplant. Hana ka hoʻokōʻana mea nui kiekie ae ma kaikaina nā mea maʻi. Aplastic anaemia i loko o nā keiki , a ua malamaia lakou nei, ma transplantation.
- Symptomatic Inc ua hoʻohana 'ia ka hakakā kekahi hoike ana mai o ka maʻi. Ua nā walaʻauʻana transfusion o ke koko eiiiiiaiou, antibiotic (lapaau "Fluconazole", "Norfloxacin") a me ka systemic antifungal Inc.
Complications a me ka hopena
- Anemic coma. No ka mea, o ka mea kokololio emi ana i loko oʻulaʻula koko aeee i ka lolo kokoke ole o oxygen ua lako, e like me ia i kaʻilihune, ka mea i nalowale ike paka, a aole e pane i ka mawaho stimuli.
- Maʻiʻaʻai.
- Hemorrhagic complications (kahe ana ke koko). Ka poʻe hewa nui pilikia - ka ai-kapaia hemorrhagic hahauʻana, i ka wa hapa o ka lolo make pono e impregnate i kona koko.
- Ka mea hōʻemi o kekahi o ka mea na nā loko (ka hapanui pinepine ia lŘlŘ ma ke alo o ka maʻi ka maʻi).
Me ua oleloia ma luna o kekahi mau o ke koa palapala hōʻoia no lapaʻau kōkua i ka lanakila i kēia pathology like anemia aplastic. Ka olelo wanana a ka hapanui maikaʻi, akā, me ka 'eleu lapaau i ke kauka wale. E like me ka loaʻa 'ikepili helu, me kūpono lapaʻau ma kahi o 90% o nā mea maʻi e make i loko o hoʻokahi makahiki.
Ka loa ka hoʻokō lapaʻau no ka iwi lolo transplantation ua ike. No ka laʻana, 9 mai o 10 hoʻomanawanuiʻana ma hope oʻoki kino ola hou ma mua o elima makahiki.
At impossibility oʻoki lāʻau lapaʻau 'uao (lāʻau Inc) no ka oi mamua o elima makahiki e hiki wale ola hapalua o ka hoʻomanawanuiʻana, a mai ka 40 makahiki.
Kāohi
Helu Kāohiʻana o ia hoʻi, ma ka hana, e pale aku adverse 'ole ma luna o ka mea likeʻole mawaho aʻe. Mākou e kamaʻilio e pili ana no walaʻauʻana mālama 'ia hoʻi i kūpono i ka AaOIeIOUIeXAOAaIN me nā kumu o ka ionizing pāhawewe, make. A eia hoi, ka mea, he pono i ka pāʻana i ka lapaʻauʻia a me ka laʻau heluna.
Secondary Kāohi (Kāohiʻana o ka mea hōʻemi o ka ua maʻi kanaka) hoʻohuʻu he dispensary kilo, e like me ka loihi o-makahiki ka hoʻoponopono lapaau.
Ma ka hopena, ka mea e e kaulana ia oe e e mai makau no ia i kaʻike,, e like me ka anemia aplastic. Photos ola kanaka, ka poe i loaa i kēia maʻi, ke hooiaio ia oe ke hana i ka pilikia. Ma keia hihia, he kūlana kūikawā e pili ana i ke kaʻina o ka imi akamai malama a me ka kānana adherence i nā koi mai kauka. E hoʻokaʻaʻike ola!
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