'O ka ma'i, 'O nā ma'i a me nā kūlana
He aha ka mea like'ole ma waena o Brugada ma'i?
Wahi a nā po'e akamai, ua ho'onohonoho'ia ka ma'i o Brugada e like me ke'ano o nā ma'i'ele'ele ma muli o ka hopena nui loa i kapa'ia he "make makehewa." 'O kēia ma'i, ma ke'ano he kūlana, ua ho'ohui pū'ia me kahi ki'eki'e o ka fibrillation ventricular, a me ka pi'i'ana o ka māhele ST.
Mana'o'ia ua'ike'ia ka ma'i o Brugada me ke alapine o 4 i ka 12% ma waena o nā hihia i loa'a i ka make koke mai nā'ano ma'i o ka ma'i. Wahi a nā po'e akamai,'o kēia ma'amau he 10 mau manawa i'oi aku ma waena o ka hapalua o ka lāhui.
Nā kumu kumu
I kēia manawa,'a'ole i a'o maika'i'ia nā hopena hope loa o kēia ma'i. Eia naʻe, kauka manaoio i ka wā 'ōewe mutations ai-kapaia "paʻakai Kanal" ka SCN5A wale o ka pahuhopu nei? Acaeoey o ka maʻi.
'O ka mea mua, pono e ho'omaopopo'ia ke'ike'ia nā hua mua, e like me ke'ano, i loko o nā kānaka ma hope o nā makahiki he kanahā. No laila, kau nā kauka i nā mea e pili nei, e hō'ike ana i ke kū'ana o ka ma'i:
- bouts o naehana kāna hana ʻano nui i ka po;
- Nā hō'ailona Syncopal;
- Nā hākoriko'o "Polyymorphic";
- Nā hua'ōlelo o ka fibrillation ventricular.
Hana
Me ka hō'ailona like'ole me Brugada syndrome, ke hō'ike mua nei ka ECG i ka hiki'ana o ke olakino o ka ma'i mai ka mea ma'amau. Ma ke'ano he lapa'au mua, nā kauka lapa'au pinepine i ka lā'au lā'au "Quinidine" a me kekahi mau mea'ē a'e, e komo pū me ka lā'au'ona "Isoproterenol". 'O ka mea hope, ua mana'o'ia he lā'au lapa'au loa e hiki ai ke ho'opau i ka "makani makani" i nā ma'i me kēia ma'i i ka pō. Ma ke'ano kumu nui o ka pale'ana i ka "make koke" o ka mea ma'i, ua'ōlelo nā kauka e ho'okomo i ka cardioverter-defibrillator. Pono e ho'omaopopo'ia inā i'ike'ia ka ma'i o Brugada, a laila i ka nele'ana o nā hō'ike waho o ka ma'i, pono ia e mālama mau'ia e nā mea lapa'au. Eia na'e,'a'ole i koi'ia ka ho'onohonoho'ia o ka cardioverter-defibrillator i hō'ike'ia i kēia lā.
I kēia manawa, ua'ike nui'ia ka ma'i o Brugada. Like kāohi ana , kauka ikaika i ka manao e undergo mau loiloi. Ho'opili ka hana i nā diagnostical diagnostics, me ka ECG, nā ho'ā'o koko, nā ho'okolohua mimi. 'O ka mea kēia,'o ia kēia mau māhele e hiki ke ho'ohana'ia no ka ho'okolokolo i ka hiki'ana o nā pilikia ma ke kino. Pono e ho'omaopopo'ia i ka kokoke'ana o nā "pili" pili loa o kēia wehewehe, pono e mālama'ia ke kūpili kūpono, a'o ka hopena e pili ana i ka wehewehe o ka "hopena o nā palena", a me ka ho'omalu o hope o ka mea ma'i no ka manawa lō'ihi e like me nā hō'ike'ike ola olakino . Ma kēia'ano wale nō, e like me ka hō'ike'ana i ka hō'ike, hiki i ka hiki ke pale i kahi hopena hopena, hiki i nā pilikia o ka hopena mahope, a me ka pale'ana i ka ma'i ma nā manawa mua o ka ulu'ana. E ola maika'i!
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