Hemolytic anaemia-Chauffard Minkowski:ʻike, a me ka lapaʻau

I anemia, i ke koko hemoglobin pae kulu ia. Me keia maʻi ma ko lākou ola i ka maka o ka hailona ana o kanaka. Eia hoʻi, 'aʻole ka mea, i na keiki uuku e pale akuʻaoʻao. Ka hapa nuiʻano likeʻole o ka maʻi i ke kumu ma ka ilihuneʻai, nele o nā wikamina, a lawe i kekahi mau lapaʻauʻia. Ma hope iho o ka hoʻopau o nā mea a pau symptoms e hoʻonāukiuki ololi paʻapū. I waena o keʻano o ka pathological keʻano o ka hanaʻana anao? Aou kekahi paʻakikī a me ka loa pilikia loa. Kēia hemolytic anaemia-Chauffard Minkowski. A e pili ana i ka mea e e kūkākūkā i kēia lā i ka 'atikala.

He aha ka anemia?

Ma lalo o anemia ia olelo maopopo e like me ka moku'āina o ke kino, wehewehe aku ma kahi nihinihi hiki emi nā hoailona o kaʻulaʻula koko keena a me hemoglobin. Kekahi mauʻano likeʻole o ka maʻi hiki aku ai i ka loli o ke kinona o ka ula koko keena. Ka mea, lilo lākou iniiaiie kuleana pili i no manawa.

Anemia ua pinepine pu ma keʻano o ka maʻi, akā,ʻaʻole loa ia iniiaiie. I mea no ke aha la oe e ole haʻalele me ka hoolohe kāna hana. He pono e like me ka hikiwawe e loaa, e imi i ka mea, a ho'āʻo e hoʻopau.

Features hemolytic anemia

Kaʻia "hemolytic anaemia" ka loaʻa o ke ākea pūʻulu o nā maʻi. A pau o ia i wehewehe aku e kekahi, he pono ole pathogenesis. Mahuahua loa ia'na o kaʻulaʻula koko aeee ke kumu no ka hoomahuahua i loko o kā lākou decomposition huahana, a me ka hoomahuahua i erythropoiesis. Loop ho okumu ua Nyos ula koko keena. Keʻano o ka hanaʻana o ko lākou lukuʻia ke kiʻekiʻe e hoomaka ana e lanakila ma luna o nā maomeka o ka muli a me ka maturation.

All haemolytic anaemia conditionally puunaueia i loko o nā pūʻulu: hereditary a me ka loaa. Ma keia 'atikala, ua loaʻa i ka piha nana ma ka mana mua. Ia e kūlike loa, ua manao ia mea he hereditary anaemia-Chauffard Minkowski.

I ka 'inikua pili pukeʻoe ke huli i kekahi mau inoa i wehewehe i ka pathological kaʻina. Kēia microspherocytic anaemia, a hereditary spherocytosis, a me ka maʻi-Chauffard Minkowski. Loa pinepine hoʻohana 'ia ka hope inoa ma nā inoa o nā kānakaʻepekema, discoverers.

I ka maʻi ua manaoia e e loa, he pono ole (1 ma kela 5 tausani. Heluna). Ua Ua diagnosedʻano nui i loko o kanaka o 'Eulopa. Ka mua hoailona i akaka i na keiki ma ka koke elemakule. Inā 'oe e ole hoʻomaka i ka hana maʻi i loko o ka' eleu kūpono no kona hopena maikaʻi 'ole ma o ka functioning o ka mea a pau meaola.

Nā kumu a me nāʻano papa hana o ka maʻi

Anemia Minkowski-Chauffard pu ma ka hana maʻamau o ke kelepona hele membranes o erythrocytes hale a me ka hana. I ka hopena o kēia mau keʻano o ka hanaʻana, e hoʻololi i kā lākou mau helehelena i ka hoʻopoepoe, e brittle. Ka mua hoailona o hemolysis - i ka make ana o kaʻulaʻula koko keena me ka i ka wā hoʻokahi kala o ka hemoglobin.

Ma ke ola i ke kanaka ulaula koko aeee i loko o kā lākou mau helehelena reminiscent o ka biconcave pā hōkū, no laila, i ka mea holo i ka uku ole ia ma ka moku. I anemia, kaʻili lahilahi kumu o ka kumuʻiʻo hoʻololi kemikala ua kupikipikio. Ua hiki aku i ka anal o ke kinowai i loko o na keena. No keia kumu, ka mea, hoʻololi 'ana i kā lākou mau helehelena. Maalo ae la oia ma ka ipu koko, ulaula koko aeee i loa ino, a ma hope o ka manawa hoʻomaka e uhai ia. E kū'ē i ke kāʻei kua o ka hoʻomauʻana keʻano o ka hanaʻana, i ka nui o kaʻulaʻula koko keena kulu dramatically, ulu hemolytic anaemia.

Inā ua mua, ua diagnosed kekahi makua me keia maʻi, ka mea, e pono e hele ma ka'āina hoʻoili no ka keiki. Loa kākaʻikahi maʻi keiki i pono ola makuahine a me Pāpā hanau. Ma keia hihia, anaemia e hoʻomōhala ana i ku e mai i ke kāʻei kua o nā loli i loko o ka DNA. Ke iniiaiie'ōewe mutation ia lŘlŘ a hiki ma fetal ulu. Elue no ka hooulu ana i ka maʻi o ka hopena ma luna o ka makuwahine o ka kino o kēia kumumea:

• pāhawewe, X-kukuna;
• intoxication me ka kaumaha metala paʻakai, narcotics, nicotine i;
• mea hoʻomaʻi hoouka.

Ma lalo o ka aoao o kēia mau kumumea e ole wale anaemia-Chauffard Minkowski, akā, i oi hoʻoponopono pathology. No laila, i hāpai keiki, i ka wahine e ho'āʻo e hoʻopale ai i kou kino.

Ka mua symptoms

Ka lapaʻau kiʻi Ua pili kēia nānā 'ia e ka oolea o ka pathological kaʻina a me ka nui o ka Hoʻololi' erythrocytes. Kona symptoms mua hiki ke malama i na keiki o ke kamaliʻi, a i ke kula makahiki. I loko o kēiaʻano o ka anaemia ana undulating. Ke kāʻili 'hemolytic ulia ia malaila mea he nui helu ana i ka wā hoʻokahi luku ana oʻulaʻula koko keena, i ukali ia e manawa o ka noho malie. Ma kēia hihia, na symptoms i ĸokoĸa ana nä pane iki.

No ka laʻana, ka mea interictal wā o ka maʻi ua hoikeia na hoailona o ka anemia. I waena o lākou nō i ka pallor o kaʻili, mucous membranes paha maka. Inā hemolytic ulia lapaʻau kiʻi ua Hoʻololi ', a ua ukali ia e na kēia symptoms:

1. Mahuahua i ka mahana i ka 38 degere, headache, malaise.
2. Ka hooulu ana o ka jaundice.
3. Pain i loko o ka abdomen, wehewehe aku spastic külana.
4. Discomfort ma ke akepaʻa, ma muli o ia kona mea ulu.
5. Li nui o ka spleen.

Hereditary hemolytic anaemia-Chauffard Minkowski loaʻa i loko o nā mākua. Ka loa pinepine ke kumu no ka imi 'inikua noonoo i keia hihia o ka yellowness o ka ili. Eia naʻe, i loko o ka hapanui o na hihia, ka maʻi i asymptomatic. E hoomanawanui i aʻo o kona ola ma ka iho a me ka IeAUPIIe, IAa IO i ka oaeouee? Nana.

Lapaʻau o keia hookolokolo ana

ʻike, o ka anemia-Chauffard Minkowski mea he mea. Inā e manaʻo ai i ka maʻi, a eia kahi mea akaka i ka loiloi mua symptoms e imi 'inikua'ōlelo aʻo. Pathology o ka hematopoietic'ōnaehana i loko o ka mākaukau o ka hematologist. Hope nana i ka hoopii o ke ahonui, a me kona ohana mōʻaukala hoʻomalu e nānā i kaʻili, a me ka sclera, hoʻomaka abdominal palpation. Muli o ia ultrasonography o ke ake, a spleen, me he symptom o ka maʻi o ka ulu i loko o ka nui o kēia mau kino.

Ka poʻe hematologist haawi ala e hiki aku ai i ka helu o ke keʻena hoʻokolohua ho'āʻo ma. Hemolytic anaemia-Chauffard Minkowski hoopaa i ke alo o ke kēia mau hoʻololi:

1. Mimi: hemoglobinuria, mahuahua kumuʻiʻo nā hoailona a me urobilin.
2. Biochemistry koko: hoemi naʻokoko, lactate dehydrogenase, ulu, hoomahuahua i kaʻauhau'ēʻaʻe bilirubin.
3. A like o kaʻulaʻula koko aeee: reticulocytosis haʻi, ka ho'ēmiʻana i loko o aeea nui, ma lalo lākou osmotic kumupaʻa.
4. General Ka Ikepili o ke koko: ESR hoʻonui, he hōʻemi iki emi ma ka platelet a me ka leukocyte ka ho'ēmiʻana waihoʻoluʻu anakahi.

Eia hoi hoʻokūpaʻa i ka ka mua ka hopena kōkua hana electrophoresis o nā polokina o ka erythrocyteʻili lahilahi i loko o ka huipūʻana a me kā lākou quantitation.

palena pauʻike,

Hemolytic anaemia Minkowski-Chauffard keiki i kekahi manawa ke kumu hihia iʻike. Kēia maʻi mea like i nā autoimmune pathologies symptoms. Nolaila, kauka ë he mähele wale no kekahi o ka kiʻiona a me ka ano no kēia 'ano o ka anemia symptoms.

Mua o nā mea a pau a mākou e kamaʻilio e pili ana i ka aaiaoe predisposition. Wale i loaʻa kekahi hihia nā makua i loa ola. Ma ka kekahi lima, i ka maʻi keiki hiki ke Hahai I he okoa loli i loko o ka iwi o ka iwipoo. Ma kanalua hihia aiiieieoaeuii ia Coombs hāpana. Inā ka Ikepili mea io, ke hoʻomanawanui ua kākoʻo anaemia-Chauffard Minkowski. ʻike, ua keia ua pau.

makeʻe kulana lapaʻau

Anemia Inc no ka mea, o kona oolea i waeʻia. Iloko o ka hoohiamoe ia, e like me ka rula, 'uao ua koi' ia. I ka pili hoouka o ka hoʻomanawanui hospitalized koke.

Makeʻe kulana lapaʻau o ka anaemia-Chauffard Minkowski nā ke kēia mau ana:

1. Hope Inc erythrocyte nuipa, ina i ke koko hemoglobin pae paka ua a hiki i ke kiʻekiʻe o ka g. 70 / ho'āo ai.
2. Albumin ua hōʻike no ka lapaau ana i kiʻekiʻe holo 'awelika o ka bilirubin.
3. No ka detoxification hoʻohana infusion Inc.
4. I ka wa e kaawale aku o ka hookahua hemolytic ka hoʻoponopono ulia wehewehe? Eaia choleretic ai '.

Ka lōʻihi like 'ole o ia Inc, i ka papa ai' a me kā lākou laʻau heluna - i hooholoia e na kauka a pau kēia mau nīnūnē ma luna o kekahi kanaka manawa.

operative uao

Inā microspherocytic hemolytic anaemia-Chauffard Minkowski e loa, makeʻe kulana hana hiki ole Makuakane me ka mea i oleloia Pahuhopu, i ka hoʻomanawanui ua manaoʻoki kino, e wehe i ka spleen. Oia i kokoke loa i kahi hiki ole loa ke hoola i ka maʻi. Ma ka kekahi lima, ma hope o ka piʻiʻana o ka helu o ka lukuiaʻulaʻula koko keena me ka nui loa hoemi a ua hooloihiia ko lakou ola kalapona.

Hemolytic ulia ma hope o ka hana ua i hou, akā, ka mea, i ka helu ana o contraindications. No ka laʻana, ana o ka spleen ua i paipai no na keiki ma lalo o 5 makahiki aie i ka mea kiʻekiʻe make kumu i loko o ka postoperative wā. Ke downside o ke kaʻina hana ua manaoia e emi i ke kino o ka ia'ku me ka pili ana i ka mea hoʻomaʻi a me ka fungal nā mea palahēhē.

I kekahi kohoʻano ua manaoia e wehe i ka spleen endovascular occlusion. 'O kēia kekahi papa hana o ka lapaʻau, e kōkua ua pinepine imi i loko o kaʻike, o "microspherocytic anaemia-Chauffard Minkowski." Iloko o ke kaʻina hana, ke kauka inserts i loko o ke kino o ka lāʻau i ka hoʻonāukiukiʻana mai o spasms, a me ka spleen hiki aku ai i ka naau hoouka. Kekahi o ka mea laila hoopakele i ka piha koko lako, a aole i lilo aku i ka hiki i ke kaua nā mea palahēhē.

hiki complications

Hemolytic anaemia-Chauffard Minkowski kamaliʻi keiki pinepine hiki aku ai i ka hoʻopaneʻe 'ia ana i loko o ka noʻonoʻo' a me ka physical? Acaeoey. No ka mea, ina i ole imi i ka makua no ka lōʻihi manawa 'inikua kōkua' ole AOON Kauka o ka aʻo.

I kanaka makua nā mea maʻi, me ka loa, he pono ole complication ua noʻonoʻo e ku e ia i ke kāʻei kua o ka gallstone mai kāna hana o ka bilirubin pūnao. Ka mea o ia ka hemolytic ulia ua pinepine ike i ka hoʻomaka o ka? Acaeoey o jaundice, no laila, ua lohi kupono lapaau. Ma ke alo o nā pōhaku i loko o ka gallbladder ua waiho ia ka cholecystectomy me ka splenectomy.

Ke kēla no ke ola

I ka emi loa mai a me ka 'eleu hana o ka hana, e wehe i ka spleen maikaʻi prognosis. Ke kala ana ia lŘlŘ koke ma hope o ka hemolytic ulia. Kona lōʻihi like 'ole hiki ke ĸokoĸa ana nä pane, akā, ma ka hapanui o na hihia mea e pili ana i mau makahiki.

aoao e pale aku

Anemia Minkowski-Chauffard mea hereditary. No laila, hiki ole i ka hanana o ka maʻi mea,ʻaʻole hiki. I mea e pale aku hanahana loa ano o ka maʻi i loko o nā mea maʻi diagnosed me keʻano o ka anaemia ka mea, ua waiho no kekahi manawa undergo piha nānā 'ana ma ke hematologist.

I ka hoʻolala i ka hāpai keiki e e hoʻomaopopo i ka likelihood o ulu i ka maʻi i loko o ka unborn keiki o 50%. No ia mea, keiki kekahi hōʻike ana ka mālamaʻana ma kekahi kauka e kuhikuhi pathologies ma ka koke ke kahua.