Hemosiderosis o ia maʻiʻaʻai: Symptoms a me ka lapaʻau

Hemosiderosis o ia maʻiʻaʻai - he maʻi loa nui. Ua lŘlŘ ka wā o ka nui o ka ulaula koko keena ma ka hui 'ana me ka'aʻaʻa o ke kanaka akemāmā. A pau keia mau mea i ka lōʻihi manawa o ka ulu ana o ka hemosiderin pigment i loaʻa ka hao.

He aha ka hemosiderosis?

E diagnose i kēia maʻi mea hiki wale nō ma luna o ka muli o X-Ray, akā naʻe, ua nui na symptoms no i kona alo hiki ke ea. Kiʻiona na hoailona i ka hoʻomanawanui gemosiderkoz maʻiʻaʻai - he ino cough, hawking mai ia i ke koko, pokole o ka hanu, kahe ana ke koko ma na maʻiʻaʻai. Aia paha ia i ka mai kuni a me tachycardia.

Ma ke kumu o ka X-Ray o ia maʻiʻaʻai kauka hiki e ke definiteʻike. i nā haʻawina i lawelawe 'ia e hōʻoia i ka hoʻomanawanui ua loaa mai keia maʻi nei. He ka ninaninau ana o sputum, koko kemika, ma ka loa a pau - akemāmā biopsy.

Lapaau ana i ka maʻi hua mai ma ke noi ana o corticosteroids a me ka ai 'e hoʻopau kekahi symptoms.

hoike ana o ka maʻi

Idiopathic pulmonary hemosiderosis ua i kapa maʻi pale purposeful-Gellerstedta. He He pathological pilikia, i hoike mai ai ia ia iho e like me ka hopena o ka kūikawā pigment hemosiderin palapala moʻopane i loko o ke kanaka akemāmā. Ke kumu nui hiʻona o keia pigment i loko o ka mea ia ia oia o ka hao'okesaside. He mea kuleana no ka papaa o ka hao i loko o ke kino. Iloko o na maʻi likeʻole ia accumulates i loko o nā nā'aʻaʻa, i hiki aku ai i ka hoʻomanawanui i ka ola pilikia. No hoi, ka mea hiki ke loaa i loko o kanaka kino.

Ma kona Kora naʻEsau, hemosiderin - 'ano apau loa waiho i loko o ke kino hoʻokoe hao. No ka mea, o keia lole i ka hai Malama Ka hue. A i kekahi kanaka e hoʻomōhala ana i idiopathic pulmonary hemosiderosis, i loko o nā nā'aʻaʻa o ke kino ke loaa mai i elima nā huna o ka hao.

E iho i ka hao hoʻomāhuahua 'aʻole i pono pili i ka functioning o ka walaʻauʻana hehee wale o ke kino, ma keia hihia ke akemāmā. Eia naʻe, ina pu ma pulmonary hemosiderosis sclerosis, ka iaea ooieoeiiaeuiiai kāna hana i loko o ke kino inevitable.

At kamepiula nā mea maʻi susceptible a hiki i kēia maʻi, he mau keiki liilii a me nā pōkiʻi. More pinepine ma mua o wahine.

Nā kumu o ka maʻi

Hemosiderosis o ia maʻiʻaʻai ke'ākoʻakoʻa i kānaka no kela kumu. Ka loa, he pono ole - he congenital hewa i loko o ka moku paia o ka pulmonary holo. No ka mea, o keia, ma ke kino, he mea he depletion o na capillaries, a me ka? Aiaiiuie cessation o ke koko. Nolaila exuded erythrocytes, a ma ka akemāmā nā'aʻaʻa e pinepine akemāmā microbleeds.

E like me ka hopena o keia hao ua hoʻokuʻuʻia, a hina i loko o ka hemosiderin. He, ma ka huli, ua kemu alveolar macrophages, a waiho ma ka epithelia a endothelial aeee i loko o ka oi nui. Pâʻani 'o ia i ke kūlana fateful o kekahi congenital kina. Hemahema pilina ma waena o nā kino, ma keia hihia - ka bronchial arteries a me aa koko o ke akemāmā.

Immunoallergic ano o ka maʻi

Kumu a me morphogenesis o ka akemāmā hemosiderosis i kekahi e immunoallergic. A pau keia'ōnaehana paleʻea eiiieaenu i poino i ka papa kuhikuhiE paia o ka pulmonary capillaries. Aia ka he 'aʻe' ana o kā lākou maʻamau hana, ma ka poino na moku koko i loko o ka maʻiʻaʻai hina oi hao, kūpono kino hana seriously kupikipikio.

Nō hoʻi, excessive palapala moʻopane o hemosiderin i loko o ka akemāmā'aʻaʻa ka poʻea pau i ka kokololio kaʻina hana o ka luku aʻulaʻula koko keena, pu ma ke kala o ka hemoglobin, a ia lŘlŘ ma ka spleen. A nui kiʻekiʻe o ka hao omo i loko o ka gut, hooloihiia hoʻohana ana ai 'me ke kiʻekiʻe hao maʻiʻo.

Ma ka loiloi mua kahua o pulmonary hemosiderosis i na keiki ke'ākoʻakoʻa me ka idiopathic maʻi i ua ole pili i nā pilikia. A hiki e ukali ia e ka maʻi pale Gainer (i loko o ka hihia ina ke kino, he ikepili koʻikoʻi i na nā polokina i kakauiaʻi ma maoli bovine waiu).

Inā hemosiderosis ia lŘlŘ hou, ke akemāmā mikrokrovotecheniya ke alakai i ka kiʻekiʻe ke koko, a hiki lilo i maʻi pilikia.

Nō hoʻi, ka maʻi i ke ukali ia e ka maʻi pale o Goodpasture. Kēia make o na alveoli o na maʻiʻaʻai a me nā konāhua, ai ukali ma kā lākou scarring. I ka maʻi, IeAUPIIe, malalo o ke kanaka elemakule 20 a hiki i 30 makahiki. Aia ka he manao e pili ana i kona hereditary ano.

stagnant hemosiderosis

Idiopathic pulmonary hemosiderosis i keiki ua pinepine triggered ma nā mea palahēhē. Ua hiki e like ka paakiki ole SARS, e like me hou nui maʻi -ʻo Waimānalo, whooping cough a me ka malaria. No hoi, ka mea hiki ia i ka hopena o ka intoxication.

Stagnant hemosiderosis e hoʻomōhala ana i loko o maʻi naʻau pilikia. Ua hiki e me ka dukima cardiac maʻi - naau maʻi, cardio a me nā maʻi.

Pinepine kumu hou a me ka stagnant hemosiderosis nei iluna hoʻopaneʻeʻia waiū ma haʻahaʻa mahana, ikaika kino ai 'ole ka noʻonoʻo' ke kanana nei, hoʻohana i kekahi lapaʻauʻia.

Inā hemosiderosis kahe ana i loko o ka alveoli o na maʻiʻaʻai, i nā kiʻi pono i nanaia ko läkou 'o microbleeds a me ka wahi excessive hoʻokomo kālā o ka hemosiderin e like me nodules, a i ka hooponopono ia, mai ka piko a hiki i ka periphery o ke akemāmā.

symptoms

Hemosiderosis kānāwai i loko o kekahi mau 'ano apau loa. Huʻi, subacute a me ka recurrent. Inā ka maʻi ua ike i na keiki, loa pinepine ia ia lŘlŘ like kakahiaka nui me kamaliʻi makahiki, no ka makahiki ekolu. Eia naʻe, loaʻa nō nā mea maʻi i loko o ka mea a kaʻike, ua waiho i loko o ka mua pule o ke ola.

Hoike aku maʻi pulmonary hemorrhage a me ka kahe ana ke koko, aloha o naehana hanu ole.

Iloko o ka hanana o complications i loko o kānaka akaka kaumaha cough Malama Ka waihoʻoluʻu a pau, ma ka loa hoopii, hiki e puʻu i ke koko. I na keiki opiopio, i ke koko hiki ia i loko o ka luaʻi.

Ma hookolokolo, kauka e lohe i ka maʻi o, tachycardia, kuni, pinepine i ka hoʻomanawanui complains o kaʻeha i loko o ka pahu a me ka abdomen, e like me ia ma na ami. Ua hiki no hoi e'āno'ē hoʻonui o ke ake, a me kaʻoi kulu i loko o ke kaumaha.

Inā hemoptysis mau no ka lōʻihi manawa, i ke ahonui e hoʻomōhala ana i anaemia, nawaliwali a me ka pōniuniu. Ka ili i kona maka, a puni na maka, aia no he ano yellowness. Ke kanaka me ka luhi koke mai a noke lohe i ka leo i loko o ka pepeiao. Kaumaha wā o ka maʻi ke'ākoʻakoʻa mai i kekahi mau hola i 10-15 lā. Nolaila, aole hiki ole ke hana me ka mālama '.

I ka wā o ka worsening cough a me ka pokole o ka hanu i emi, akā, e ka paakiki ole i pai mai ai, e ike i ke kauka ua koi koke. Ma ka hoʻopiʻi kala i ole e loaʻa i nā mea a pau, a me ke kanaka ke alakai i ka piha ola workable.

Me kēlā me kēia exacerbation o ka maʻi kala manawa ua hoemi, akā, no ka like ana, e hoʻomāhuahua i ka lōʻihi like 'ole a me ka oolea o crises. Kekahi o na hopena o ka anaemia - ka huina depletion o ke kino. Ma pohihihi keia hoopii, he hiki i ka make ana o ka hoʻomanawanui - he kaumaha hoʻokūkū ke hiki mai, no ka huʻi pulmonary hemorrhage a me ka manawa e naehana hanu ole.

ʻike, hemosiderosis

I mea e pololei diagnose pulmonary hemosiderosis, e pono i ka makaukau manao o kekahi mau mākaukau. Mua o nā mea a pau, e ka pulmonologist, hematologist. A me kekahi pono, e noiʻi i ka lapaʻau hoike ana mai o ka maʻi. Hiki ole ke hana me ke ao o ka X-kukuna, sputum Ka Ikepili, ke koko (me kekahi mau Ka Ikepili, a me biochemical) a me ka akemāmā biopsy.

E diagnose i kēia maʻi mea paʻakikī loa. Pinepine lawe mahina a hiki makahiki mua akamai onoho ana i kaʻike,. I kekahi manawa, hahao aku la ia posthumously. Ka mea o ia ka mea mua mea i kekahi symptoms, like i ka nui no hoi na maʻi, a me na mea he nui wale, mai haawi ia waiwai. IeAUPIIe, IAa IO ka mea, O like he naehana maʻi pū ma ka cough a me ka anaemia.

huʻi pae

Inā kauka diagnosed idiopathic pulmonary hemosiderosis, lapaʻau mea pono. Ke kino iho hiki ole Makuakane me kēia pilikia. Ma ka huʻi ano o ka maʻi ua pu ma crackles a me palpitations. I ka Ia manawa hoemi ia i ka nui o kaʻulaʻula koko keena, ke kiekie bilirubin pae o ka lāʻau lapaʻau hao i loko o ke koko o ka palena haʻahaʻa.

Ma crises ana leukocytosis, ESRʻilikai, a hookuu Hōʻike ka li nui. Ma nā kahua o ka hoʻonaʻauao ma hope o ka maʻi i Konakele. Polycythemia. He He benignʻeho kaʻina hana, pu ma hyperplasia o ka iwi lolo keena.

X-Ray haʻawina

Ma ka like o ka X-na kukuna ma na kuʻina kakahiaka o ka maʻi wehewehe aku ma ka emi o ka mäliko o ke akemāmā mahinaʻai. I ka Ia manawa, i ke kolu a me ka ha kahua o ka hoʻonaʻauao i ae nānā mau, pili poeleele hoi a me lesions o connective'aʻaʻa me ka ano scars.

Pinepine eia hou mea nui malumalu, hoʻowahāwahā i ka mea i ka mea kahiko nalo ia. Ma spirography nohoaliʻi naehana pilikia, ma ka electrocardiogram - miokardiostrofiya. Hopeʻike, kōkua akemāmā biopsy.

hemosiderosis lapaʻau

Holomua lapaʻau o keia maʻi mea wale nō e hiki ka wā lōʻihi-makahiki lapaʻau papa o corticosteroids. No ka laʻana, "Prednisolone" kōkua hoola pulmonary hemosiderosis. Ke k minimizes ka permeability o na moku koko, a inhibits ka hooulu ana o autoimmune reactions.

Inā makeʻe kulana kūlana kanaka i 'ike' ia e ineffective, lailaʻoki lāʻau lapaʻau ki ina hana like i hoʻohana. Hiki ke hoomaopopo a hapa 'ia' weheʻia ka spleen, ka mea hiki me ka nui loa emi i ka pilikia o remissions. Nō hoʻi ka mea, ho'ēmi i kā ka likelihood o crises, a, e hoomahuahua i ka hoʻomanawanui ka ola expectancy ma hope o kēia hana ma 7-10 makahiki.

Hoomakaukau i loko o ka huʻi pae o ka maʻi ulu

He noteworthy i loko o ka huʻi pae, a ma ka Kāohiʻana o like ai 'i hoakaka ia. A hiki i kaʻike, o "pulmonary hemosiderosis" ana hana pono ma o ka hoʻohui pū ana i cytostatic konohiki a me ka plasmapheresis. Kēia ho'ēmi i kā ka meaʻikeʻia o ka hou autoantibodies, a kōkua i ke kino Makuakane me ka mea kahiko.

Ua mea no hoi i ka hoʻokō iaoia - ana o ka hao i loko o ka mimi, ua hoʻohana 'ia no kēia infusion "Desferal". Ma ka iapaau ana o symptoms hoʻohana bronchodilators, antikoagulyarnye 'o ia hoʻi.

Lōʻihi-ʻia ke kala ana i kahuna lapaau e hoʻokō, oiai no lākou nā mea maʻi i ka ikaikaʻai i ka neʻe aku a pau me nā huahana nānā 'ana i lepo bipi no ka waiū. Inā ka maʻi kahe i loko o ka maʻi ke kahua, paha ka manawa i oleloia o nitrates. ka mea, ua oi loa aku hoi me ka maʻi naʻau pilikia pili.

ano hemosiderosis

Kauka i kekahi mauʻano likeʻole o kēia maʻi. Ma kekahi, pulmonary hemosiderosis wehewehe aku (macropreparations "Brown induration malamalama"). Ma kēia hihia, na ia maʻiʻaʻai mahuahua i nui, i ka loa anuanu hionapāʻili. No hoi, pouli-ula i eleele i kokoke ma ka mahele kekahi 'whitish, ahu iho a me ka brownish inclusions.

Ua hiki no hoi i hoʻomaka ai hemosiderosis akemāmā (micropreparations № 111). Ma keia hihia,ʻeleʻele pigments hiki i loko o na keena, a mawaho mea i keʻena hoʻokolohua naoh Perls lilo uliuli a he omaomao iki. Ka mea, e ala aʻeʻoe ma waena o ka bronchi a me ka alveoli cavities.

A, i kēia mau kīʻaha i kanaka akemāmā ka loa hoonee aku, a congested. I ka maʻi ua pu e nui kahe ana ke koko i loko o ka paku ma waena o nā alveoli. I ka Ia manawa ka mea, e wehe ahu iho la ka connective'aʻaʻa.