Klippel-Trenaunay maʻi pale: Hawaii photo, symptoms, lapaʻau

More iiiaanoaa mai hana embryonic wā. No laila, o ka hopena ma luna o lākou e ulu ai ke ole mau loa ana. Ma hope o nā mea a pau, ka hapanui o kēia mau abnormalities i diagnosed hanau i ke keiki i ka ma hope wale nō. A me kekahi mau mea hope. No kekahi o ka aaiaoe maʻi e loaʻa Klippel-Trenaunay maʻi. Ka maʻi pale i loaa i loko o ke kakahiaka nui 20th kenekulia. Keia ua wahi i ka muli o ka 'epekema o aaiaoe?. Pinepine i ka maʻi susceptible kane. Naʻe, ka mea, ua i loaʻa i waena o ka wahine heluna. Pathology wahi i congenital vascular kāna hana.

maʻi pale, Klippel-Trenaunay Description

Klippel-Trenaunay maʻi pale ua noʻonoʻo i ke nānā aaiaoe kina. Wńnana i ka hooulu ana o keia pathology mea kokoke hiki ole, no ka mea, ka mea kina mea pohihihi keia, a ka mea ua ole diagnosed i hāpai keiki. Naʻe, i loko o kekahi mau hihia, i ka maʻi hiki ke kēia Klippel-Trenaunay. Ka maʻi pale pili i ka hereditary maʻi. Nolaila, aaiaoe Ka Ikepili E hoʻokuleana i hapai wahine i loko o ka ohana ma na hihia o keia maʻi mai ai. Kekahi inoa no ka maʻi - hypertrophic hemangiectasia. Ka lapaʻau kiʻi Klippel-Trenaunay maʻi pale kikowaena ka papa kuhikuhiE symptoms ekolu:

1. Varicose aa koko.
2. Keʻano o ka makahiki pūkoʻa ia ma luna o kaʻili.
3. Hoʻololi i ke akea a me ka lōʻihi o ka loli ana o ka lala.

Ma kekahi hihia o skeletal a me ka pahee'aʻaʻa hypertrophy i malama. Pinepine pathology wehewehe aku e holumua ai papa. Ke prognosis hilinaʻi nui ma luna o ka oolea o vascular hou. Oiai ke kumu o ka maʻi,ʻaʻole hiki ke eliminated, pākōlea ana, e kōkua hoʻoikaika i ka pono o ke ola o ka hoʻomanawanui. People loaa mai keia maʻi ua ia he kīnā o ke kino.

Kumu o Klippel-Trenaunay maʻi pale

No kekahi kumu, he mea he maʻi Klippel-Trenaunay? Ka maʻi pale e hoʻomōhala ana i like me ka hopena o ka aaiaoe kina. Kēia anomaly ua pū i hiki i ka autosomal Hoʻohaku hooilina type. Kēia 'o ia hoʻi ia ina he mea ia he aaiaoe hewa i loko o kekahi o na makua, aia no he manawa kūpono o ka maʻi pale i loko o ke keiki, he 50%. Nō hoʻi, i ka maʻi hiki e pū i hiki ma kekahi hanauna, i mea - mai nā kūpuna mai. Ma keia hihia, no ka pahiki o 25%.

Like a pau aaiaoe abnormalities, vascular mā hoʻomōhala i ka fetal'aʻaʻa lepe puke. Ua hiki ke loli 'ole i kaʻino wale i. Mau nā kumumea like me:

1. Manaʻoʻike discomfort i loko o ka mua mau pule o ka hāpai keiki.
2. Infectious maʻi. O ka nui i maʻi mea hoʻomaʻi lesions o ke kino.
3. Ka hoʻohanaʻana i ai 'me ka teratogenic waiwai.
4. Komo ai 'koke ma mua hapai ana, a i hāpai keiki.
5. Puhi paka a me ka alcoholism.
6. Air haumia ea ma kaʻawahia waiwai, pāhawewe.

A pau o kēia mau kumumea hiki i loli i loko o ke kino o na wahine, a me ka unborn keiki. Ka mea, ua oi loa pilikia i loko o ke kahua o ka hoʻonaʻauao kakahiaka o ka hāpai keiki. Ma hope o nā anomalies hiki e ua loaʻa i loko o kēia wā.

ʻano papa hana o ka maʻi

No ke aha la he mea vascular loli ka maʻi Klippel-Trenaunay? Ka maʻi pale hoike mai ai ia lakou i na hoailona o venous kāna hana. Keʻano papa hana o ka? Acaeoey o pathology ma ka paleʻana i ke outflow o ke koko mai ka laloʻaoʻao. O ke kumu ho i ka mea i ka venous lumen ua hou, aia no he mīkini'opihia o ka arterial lala moku, hypertrophied Muscle, koena embryonic'aʻaʻa. Ma muli o ka 'aʻe' ana i ka outflow o ke koko, he mea hypertension. Vienna ua i nā thinned, paku ole ia i pōʻino. Eia hou kekahi, o Nyos ana o ka nohona kiwikā nakeke. Ma muli o ke koko stasis lala hoʻomaka i ka hypertrophy. Aie i ka stagnation i ae trophic kuleana pili i. Nolaila,'aʻaʻa paku ole ia i ischemia. Hooloihiia mai ka pioloke o ke koko lako hiki aku ai i ka sclerosis. Kahi I'aʻaʻa hypertrophy ia lŘlŘ hyperemia a me ka edema. Ma kekahi mau hihia, e malama, e hoʻololi a me nā iwi. Nolaila pōniuniu wale ia e kekahi lala e ole mahuahua wale ma ka laula, akā, i hooloihi ai.

Klippel Trenaunay Syndrome-: symptoms

Ma ka hoikeana o Klippel-Trenaunay maʻi pale nā loli ole wale ma ka aoao o ka venous oihana, akā, 'ē aʻe mā. I loko nō o ka mea i congenital abnormality, e hōʻike i ka mua symptoms ma adolescence ole adulthood. Ke'ōlelo mai, no ka lapaʻau hoikeana loaʻa nā kēia aʻe ':

1. Dilation o superficial wāwae aa koko. Ua hoike mai ai ia pathological kinking a me kaʻeha a ka moku hiki i ka maka kapa ole. Ma ka hapanui o na hihia varicose aa koko aia ma luna o ka pā ili o nā wāwae.
2. Ka hua i loko o ka nui o ka lala. Pinepine pu ma ka hoʻoʻino hanana. Ma muli o ke koko stasis loli wāwae i e loa okoa mai ka olakino lala. Pinepine ia mea hyperemic, ai hanaʻia naʻe ili.
3. Lala hooloihiia mai. Hypertrophy e hiki nā wāwae a me nā lima.
4. Keʻano o ka pigmented nevi ma luna o kaʻili. Ma kekahi ala e, i kapa mau me ka ho okumu "waina kohu".

Nō hoʻi, a me ka Holomua o ka maʻi ikea trophic loli. ulcerative mā ke'ākoʻakoʻa i loko o ka loli wahi, a e ole hoola no ka lōʻihi manawa. I waena o nā abnormalities ulu ana ma keia pathology, he mea polydactyly, i ke alo o ka fused interconnected manamana lima a me nā manamana wāwae.

Pehea e diagnose i ka maʻi Klippel-Trenaunay?

Maʻi paleʻike, o Klippel-Trenaunay ua pinepine ka nānā 'ana ma luna o lapaʻau hoike ana. Symptoms o ka maʻi e hōʻike i nā. Ka hoailona mua e lilo ana i ke ano o ka "waina kohu" a me aa koko. Inā e hui me ka hypertrophy o ka lala mau symptomsʻanaʻike,: Klippel-Trenaunay maʻi pale. Photos o kanaka e loaa ana mai i kēia maʻi i like i kekahi i kekahi. Ka mea, hiki ke 'ike i loko o ka moʻokalaleo hoolilo i pohihihi keia aaiaoe pathologies. Nolaila, hapanuiʻike nei,ʻaʻole paʻakikī.

Ma waho aʻeo no ka lapaʻau ikepili, hana venography, ultrasonography o ka lalo lala, X-kukuna.

Klippel Trenaunay Syndrome-: lapaau o ka maʻi

ka hana ua noʻonoʻo i ka nui 'inikua kekahi hanana. Ka buke o ka 'uao me ka nānā' ana i ka degere o vascular lesion. E hoʻonui i ka lumen o ke aa koko stenting ua hana. I ka wa o ka nui 'āpana o ka luku produces holo alaʻokoʻa moku - ke kūapoʻana ia me ka e kanu pūʻia paena.

E hakakā varicose hoonohoia skleroteropiya, kukuna coagulation o aa koko. E hoomanawanui i loaa mai i kēia maʻi, e mae wale pono mīkini'opihia huihui.

maʻi pale, Klippel-Trenaunay Kāohi

Klippel-Trenaunay maʻi pale i na kamalii uuku ua kākaʻikahi diagnosed. Pinepine ka mea, ua 'akomi i loko o na mahina mua paha makahiki o ke ola. E pale maʻi, ia mea pono ke hoomalu ia lakou iho, mai ka palapala ole i hāpai keiki. Kekahi kāohi ana ua manaoia e e he aaiaoe ninaninau o ka fetus ma ke alo o ka hihia o ka maʻi i loko o ka 'ohana.